An autopsy case of Degos' disease with ascending thoracic myelopathy

Clinical Neurology

Volumn 38, Issue 12, 1998, Pages 1049-1053

  Sugai, Fuminobu ^a   Sumi, Hisae ^a,b   Hara, Yasuo ^a   Kajiyama, Koji ^a   Morino, Hideo ^a   Fujimura, Harutoshi ^b  

^a KANSAI ROSAI HOSPITAL   (Japan)

^b OSAKA UNIVERSITY MEDICAL SCHOOL   (Japan)

Author keywords

Degos' disease; Myelopathy; Steroid pulse dose therapy

Indexed keywords

CYCLOPHOSPHAMIDE; METHYLPREDNISOLONE; OZAGREL;

ADULT; ARTERY INTIMA PROLIFERATION; ARTICLE; AUTOPSY; CASE REPORT; CEREBROSPINAL FLUID CYTOLOGY; COMA; GAIT DISORDER; HUMAN; HUMAN TISSUE; INTRAVENOUS DRUG ADMINISTRATION; MALE; MALIGNANT ATROPHIC PAPULOSIS; OPHTHALMOPLEGIA; ORAL DRUG ADMINISTRATION; PROTEIN CEREBROSPINAL FLUID LEVEL; RESPIRATORY FAILURE; SPINAL CORD DISEASE; STEROID THERAPY; TISSUE NECROSIS; TREATMENT FAILURE;

ADULT; CENTRAL NERVOUS SYSTEM; DIGESTIVE SYSTEM; DISEASE PROGRESSION; HUMANS; MALE; MYELITIS, TRANSVERSE; RESPIRATORY INSUFFICIENCY; SKIN; SKIN DISEASES, PAPULOSQUAMOUS; SKIN DISEASES, VASCULAR;

EID: 0032435547     PISSN: 0009918X     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

References (23)

1. Köhlmeier W . Multiple Hautnekrosen bei Thrombangiitis obliterans. Arch Dermatol Syphilol 181 : 783-792, 1941
2. Degos R, Delort J. Tricot R : Dermatite papulo-squameuse atrophiante. Bull Soc Fr Dermatol Syphiligr 49 : 148-150, 1942
3. Degos R : Malignant atrophic papulosis. Br J Dermatol 100 : 21-35, 1979
4. Snow JL, Muller SA : Degos syndrome : malignant atrophic papulosis. Sem Dermat 14 : 99-105, 1995
5. Blecic S, Bogousslavsky J : Kohlmeier-Degos disease (malignant atrophic papulosis). In Stroke, 2 nd ed, ed. by Barnette HJM, Mohr JP, Stein BM, et al. Churchill Livingstone, 1992. pp 448-452
6. Subbiah P, Wijdicks E, Muenter M, et al : Skin lesion with a fatal neurologic outcome (Degos' disease). Neurology 46 : 636-640, 1996
7. Culicchia CF, Gol A, Erickson EE : Diffuse central nervous system involvement in papulosis atrophicans maligna. Neurology 12 : 503-509, 1962
8. McFarland HR, Wood WG, Drowns BV, et al : Papulosis atrophicans maligna (Kohmeier-Degos disease) : a disseminated occlusive vasculopathy. Ann Neurol 3 : 388-392, 1978
9. McFarland HR : Malignant atrophic papulosis (Kohlmeier-Degos disease). In Handbook of clinical neurology, ed by Vinken PJ, Bruyn GW, Klawans HL, et al, vol 39, Neurological manifestations of systemic diseases, Elsevier, Amsterdam, 1980, pp 435-448
10. Label LS, Tandan R, Albers JW : Myelomalacia and hypoglycorrhachia in malignant atrophic papulosis. Neurology 33 : 936-939, 1983
11. Burrow JN, Blumbergs PC, Iyer PV, et al : Kohlmeier-Degos disease : a multisystem vasculopathy with progressive cerebral infarction. Aust NZ J Med 21 : 49-51, 1991
12. Howsden SM, Hodge SJ, Herndon JH, et al : Malignant atrophic papulosis of Degos. Arch Dermtol 112 : 1582-1588, 1976
13. Stahl D, Thomsen K, Hou-Jensen K : Malignant atrophic papulosis. Treatment with aspirin and dipyridamole Arch Dermatol 114 1687-1689, 1978
14. Tribble K, Archer ME, Jorizzo JL, et al : Malignant atrophic papulosis : absence of circulating immune complexes or vasculitis. J Am Acad Dermatol 15 : 365-369, 1986
15. Vazquez-Doval FJ, Ruiz de Erenchun F, Paramo JA, et al : Malignant atrophic papulosis. A report of two cases with altered fibrinolysis and platelet function. Clin Experi Dermat 18 : 441-444, 1993
16. Sotrel A, Lacson AG, Huff KR : Childhood Kohlmeier-Degos disease with atypical skin lesions. Neurology 33 : 1146-1151, 1983
17. Drucker CR : Malignant atrophic papulosis : response to antiplatelet therapy. Dermatologica 180 : 90-92, 1990
18. Englert HJ, Hawkes CH, Boey ML, et al : Degos' disease : association with anticardiolipin antibodies and the lupus anticoagulant Br Med J 289 : 576, 1984
19. Assier H, Chosidow O, Piette JC, et al : Absence of antiphospholipid and anti-endothelial cell antibodies in malignant atrophic papulosis : a study of 15 cases. J Am Acad Dermatol 33 : 831-833, 1995
20. Roach ES : Malignant atrophic papulosis (Kohlmeier-Degos disease). In Handbook of clinical neurology, ed by Toole JF, vol 11 (55). Elsevier, Amsterdam, 1989, pp 275-281
21. Katz SK, Mudd LJ, Roenigk HH : Malignant atrophic papulosis (Degos' disease) involving three generations of a family. J Am Acad Dermatol 37 : 480-484, 1997