Recombinant caprine 3H-[N-acetylglucosamine-6-sulfatase] and human 3H- [N-acetylgalactosamine-4-sulfatase]: Plasma clearance, tissue distribution, and cellular uptake in the rat

Journal of Molecular Neuroscience

Volumn 11, Issue 3, 1998, Pages 223-232

  Jones, Margaret Z ^a,b   Brumfield, Leanne K ^a   King, Barbara M ^a   Hopwood, John J ^a   Byers, Sharon ^a  

^a WOMEN S AND CHILDREN S HOSPITAL   (Australia)

^b MICHIGAN STATE UNIVERSITY   (United States)

Author keywords

Caprine N acetylglucosamine 6 sulfatase; Human N acetylgalactosamine 4 sulfatase; Lysosomal storage diseases; MPS IIID; MPS VI; Recombinant lysosomal enzymes

Indexed keywords

CAPRINE N ACETYLGLUCOSAMINE 6 SULFATASE; N ACETYLGALACTOSAMINE 4 SULFATASE; SULFATASE; UNCLASSIFIED DRUG; GALNS PROTEIN, HUMAN; MANNOSE 6 PHOSPHATE; MANNOSE PHOSPHATE; MANNOSE-6-PHOSPHATE; PROTEIN PRECURSOR; RECOMBINANT PROTEIN; SOMATOMEDIN B RECEPTOR;

ANIMAL CELL; ARTICLE; ENZYME MODIFICATION; ENZYME REPLACEMENT; LYSOSOME STORAGE DISEASE; MAROTEAUX LAMY SYNDROME; NONHUMAN; PLASMA CLEARANCE; RAT; RECEPTOR AFFINITY; SANFILIPPO SYNDROME; STRUCTURE ACTIVITY RELATION; TISSUE DISTRIBUTION; AFFINITY CHROMATOGRAPHY; ANIMAL; BINDING COMPETITION; BRAIN; CELL CULTURE; CHEMISTRY; CYTOLOGY; DRUG EFFECT; ENZYMOLOGY; GOAT; HALF LIFE TIME; HUMAN; ISOLATION AND PURIFICATION; LIVER; METABOLISM; PROTEIN BINDING;

ANIMALS; BINDING, COMPETITIVE; BRAIN; CELLS, CULTURED; CHONDROITINSULFATASES; CHROMATOGRAPHY, AFFINITY; GOATS; HALF-LIFE; HUMANS; LIVER; LYSOSOMAL STORAGE DISEASES; MANNOSEPHOSPHATES; N-ACETYLGALACTOSAMINE-4-SULFATASE; PROTEIN BINDING; PROTEIN PRECURSORS; RATS; RECEPTOR, IGF TYPE 2; RECOMBINANT PROTEINS; TISSUE DISTRIBUTION;

EID: 0032216845     PISSN: 08958696     EISSN: None     Source Type: Journal    
DOI: 10.1385/JMN:11:3:223     Document Type: Article

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