Impaired aerobic glycolysis in muscle phosphofructokinase deficiency results in biphasic post-exercise phosphocreatine recovery in 31P magnetic resonance spectroscopy

Neuromuscular Disorders

Volumn 8, Issue 7, 1998, Pages 480-488

  Grehl, T ^a   Muller K ^b   Vorgerd, M ^a   Tegenthoff, M ^a   Malin, J P ^a   Zange, J ^b  

^a RUHR UNIVERSITY BOCHUM   (Germany)

^b GERMAN AEROSPACE CENTER DLR   (Germany)

Author keywords

Differential diagnosis; Energy metabolism; Magnetic resonance spectroscopy; Phosphocreatine; Phosphofructokinase deficiency; Post exercise recovery; Skeletal muscle; Tarui's disease

Indexed keywords

6 PHOSPHOFRUCTOKINASE; ADENOSINE TRIPHOSPHATE; CREATINE PHOSPHATE;

ADULT; ARTICLE; CASE REPORT; ENERGY METABOLISM; ENZYME DEFICIENCY; EXERCISE; FEMALE; GASTROCNEMIUS MUSCLE; GLYCOLYSIS; HETEROZYGOTE; HUMAN; HUMAN EXPERIMENT; MALE; NORMAL HUMAN; NUCLEAR MAGNETIC RESONANCE; PRIORITY JOURNAL;

ADENOSINE TRIPHOSPHATE; ADULT; AEROBIOSIS; AGED; EXERCISE TEST; FEMALE; GLYCOGEN STORAGE DISEASE TYPE VII; GLYCOLYSIS; HETEROZYGOTE; HOMOZYGOTE; HUMANS; MAGNETIC RESONANCE SPECTROSCOPY; MALE; MIDDLE AGED; MUSCLE, SKELETAL; PHOSPHOCREATINE; PHOSPHORUS ISOTOPES;

EID: 0032190897     PISSN: 09608966     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0960-8966(98)00066-2     Document Type: Article

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