Accelerated linear growth and advanced bone age in Sotos syndrome is not associated with abnormalities of collagen metabolism

Clinical Biochemistry

Volumn 31, Issue 4, 1998, Pages 241-249

  Rao, Velidi H ^a   Buehler, Bruce A ^a   Schaefer, G Bradley ^a  

^a UNIVERSITY OF NEBRASKA MEDICAL CENTER   (United States)

Author keywords

Collagen degradation; Collagen metabolism; Collagen production; Collagen turnover; Fibroblasts; Gene expression; RT PCR; SDS PAGE; Sotos syndrome; Type I collagen

Indexed keywords

COLLAGEN; COLLAGENASE;

ADOLESCENT; ARTICLE; BONE AGE; BONE GROWTH; CASE REPORT; CHILD; COLLAGEN DEGRADATION; FEMALE; GENE EXPRESSION REGULATION; HUMAN; HUMAN TISSUE; MALE; POLYACRYLAMIDE GEL ELECTROPHORESIS; PRIORITY JOURNAL; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; SCHOOL CHILD; SKIN FIBROBLAST; SOTOS SYNDROME;

ADOLESCENT; AGE DETERMINATION BY SKELETON; CELLS, CULTURED; CHILD; COLLAGEN; COLLAGENASES; CRANIOFACIAL ABNORMALITIES; EDETIC ACID; FEMALE; FIBROBLASTS; GELATINASES; GROWTH DISORDERS; HUMANS; MALE; MATRIX METALLOPROTEINASE 2; MATRIX METALLOPROTEINASE 9; METALLOENDOPEPTIDASES; PROCOLLAGEN; PROTEIN STRUCTURE, SECONDARY; RNA, MESSENGER; SYNDROME;

EID: 0032101633     PISSN: 00099120     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0009-9120(98)00023-X     Document Type: Article

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