Effect of vitamin B6 supplementation in McArdle's disease: A strategic case study

Neuromuscular Disorders

Volumn 8, Issue 3-4, 1998, Pages 210-212

  Phoenix, Joanne ^a   Hopkins, Pam ^b   Bartram, Clare ^b   Beynon, Robert J ^b   Quinlivan, Rosaline C m ^a   Edwards, Richard H t ^a  

^a Neuroendocrine and Obesity Biol U   (United Kingdom)

^b UNIVERSITY OF MANCHESTER   (United Kingdom)

Author keywords

McArdle's disease; Myophosphorylase deficiency; Pyridoxine; Therapy; Vitamin B6

Indexed keywords

PYRIDOXINE;

ADULT; CASE REPORT; CLINICAL TRIAL; CONFERENCE PAPER; CONTROLLED CLINICAL TRIAL; CONTROLLED STUDY; DIET SUPPLEMENTATION; EXERCISE TOLERANCE; GLYCOGEN STORAGE DISEASE TYPE 5; HUMAN; MALE; MUSCLE CRAMP; MUSCLE FATIGUE; MUSCLE FORCE; MUSCLE FUNCTION; PRIORITY JOURNAL; SINGLE BLIND PROCEDURE; VITAMIN BLOOD LEVEL;

EID: 0032078665     PISSN: 09608966     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0960-8966(98)00004-2     Document Type: Conference Paper

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4. 6 metabolism examined in miniature swine by continuous administration of pyridoxine. In: Canolty NL, Cain TP, editors. Mathematical models in experimental nutrition. Athens, GA: University of Georgia, Academic Press, 1985:99-111.
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8. McConchie S.M., Coakley J., Edwards R.H.T., Beynon R.J. Molecular heterogeneity in McArdle's disease. Biochim Biophys Acta. 1096:1991;26-32.