Long-term prognosis of surgically-treated aortic aneurysms and dissections in patients with and without Marfan syndrome

European Journal of Cardio-thoracic Surgery

Volumn 13, Issue 4, 1998, Pages 416-423

  Detter, Christian ^a,b   Mair, Helmut ^a   Klein, Hanns Georg ^a   Georgescu, Carmina ^a   Welz, Armin ^a   Reichart, Bruno ^a  

^a LUDWIG MAXIMILIANS UNIVERSITY   (Germany)

^b GOETHE UNIVERSITY   (Germany)

Author keywords

Aortic aneurysm; Connective tissue; Fibrillin; Marfan syndrome; Redissection

Indexed keywords

FIBRILLIN;

ADULT; AORTA ANEURYSM; AORTA DISSECTION; AORTA SINUS; AORTA SURGERY; ARTICLE; COMPOSITE SKIN GRAFT; CONNECTIVE TISSUE DISEASE; FEMALE; GENETIC LINKAGE; HIGH RISK POPULATION; HUMAN; MAJOR CLINICAL STUDY; MALE; MARFAN SYNDROME; PRIORITY JOURNAL; PROGNOSIS; REOPERATION;

ADULT; ANEURYSM, DISSECTING; AORTIC ANEURYSM, THORACIC; FEMALE; HUMANS; MALE; MARFAN SYNDROME; MIDDLE AGED; PROGNOSIS; RECURRENCE; REOPERATION; RETROSPECTIVE STUDIES; SURVIVAL ANALYSIS; TREATMENT OUTCOME;

EID: 0032051959     PISSN: 10107940     EISSN: None     Source Type: Journal    
DOI: 10.1016/S1010-7940(98)00043-8     Document Type: Article

References (37)

1. [1] Pyeritz RE, McKusick VA. The Marfan syndrome: diagnosis and management. New Engl J Med 1979;300:772-7.
2. [2] Sakai LY, Keene DR, Engvall E. Fibrillin: a new 350-kD glycoprotein, is a component of extracellular microfibrils. J Cell Biol 1986;103(6):2499-509.
3. [3] Kainulainen K, Pulkkinen L, Savolainen A, Kaitila I, Peltonen L. Location on chromosome 15 of the gene defect causing Marfan Syndrome. New Engl J Med 1990;323:935-9.
4. [4] Tsipouras P, Del Masreo R, Safarazi M, Lee B, Vitale E, Child AH, Godfrey M, Devereux RB, Hewett D, Steinmann B, Viljoen D, Sykes BC, Kilpatrick M, Ramirez F. Genetic linkage of Marfan syndrome, ectopia lentis, and congenital contractural arachnodactyly to the fibrillin genes on chromosomes 15 and 5. New Engl J Med 1992;326:905-9.
5. [5] Dietz HC, Cutting GR, Pyeritz RE, Maslen CL, Sakai LY, Corson GM, Puffenberger EG, Hamosh A, Nanthakumar E, Curristin S, Stetten G, Meyers DA, Francomano CA. Defects in the fibrillin gene cause the Marfan syndrome: linkage evidence and identification of a missense mutation. Nature 1991;352:337-9.
6. [6] Lee B, Godfrey M, Vitale E, Hori H, Mattei M-G, Safarazi M, Tsipouras P, Ramirez F, Hollister DW. Linkage of Marfan Syndrome and a phenotypically related disorder to two different fibrillin genes. Nature 1991;352:330-4.
7. [7] Magenis RE, Maslen CL, Smith L, Allen L, Sakai LY. Localization of the fibrillin (FBN) gene to chromosome 15, band q21.1. Genomics 1991;11:346-51.
8. [8] Dietz HC, Pyeritz RE, Hall BD, Cadle RG, Hamosh A, Schwartz J, Meyers DA, et al. The Marfan syndrome locus: confirmation of assignment to chromosome 15 and identification of tightly linked markers at 15q15-q21.3. Genomics 1991;9:355-61.
9. [9] Habbal MHE. Cardiovascular manifestations of Marfan's syndrome in the young. Am Heart J 1992;123(3):153-7.
10. [10] Halpern BL, Char F, Murdoch JL, McKusick VA. A prospectus on the prevention of aortic rupture in the Marfan Syndrome with data on survivorship without treatment. Hopkins Med J 1971;129:123-9.
11. [11] Murdoch JL, Walker BA, Halpern BL, Kuzma JW, McKusick VA. Life expectancy and causes of death in the Marfan Syndrome. New Engl J Med 1972;286:804-8.
12. [12] DeBakey ME, McCollum H, Crawford ES. Dissection and dissecting aneurysms of the aorta: twenty-years follow-up of five hundred twenty-seven patients treated surgically. Surgery 1982;92:1118.
13. [13] Beighton P, DePaepe A, Danks D, Finidori G, Gedde-Dahl T, Goodman R, Hall JG. International nosology of heritable disorders of connective tissue, Berlin, 1986. Am J Med Genet 1988;305:581-94.
14. [14] Shores J, Berger KR, Murphy EA, Pyeritz RE. Progression of aortic dilatation and the benefit of long-term ß-adrenergic blockage in Marfan's syndrome. New Engl J Med 1994;330:1384-5.
15. [15] Bentall H, De Bono A. A technique for complete replacement of the ascending aorta. Thorax 1968;23:338-9.
16. [16] Wheat MW, Wilson JR, Bartley JD. Successful replacement of the entire ascending aorta and aortic valve. J Am Med Assoc 1964;188:717.
17. [17] Kaplan E, Meier P. Non parametric estimation from incomplete observations. J Am Stat Assoc 1953;53:457.
18. [18] Smith JA, Fann JI, Miller DC, Moore KA, DeAnda A, Mitchell RS, Stinson EB, Oyer PE, Reitz BA, Shumway NE. Surgical management of aortic dissection in patients with the Marfan Syndrome. Circulation 1994;90(Part II):II-235-42.
19. [19] Gott VL, Pyeritz RE, Magovern GJ, Cameron DE, McKusick VA. Surgical treatment of aneurysms of the ascending aorta in the Marfan Syndrome. New Engl J Med 1986;314:1070-4.
20. [20] Gott VL, Pyeritz RE, Cameron DE, Greene PS, McKusick VA. Composite graft repair of Marfan aneurysm of the ascending aorta: results in 100 patients. Ann Thorac Surg 1991;52:38-45.
21. [21] Crawford ES. Marfan's syndrome: broad spectral surgical treatment cardiovascular manifestations. Ann Surg 1983;198:487-505.
22. [22] Crawford ES, Coselli JS, Svensson LG, Safi HJ, Hess KR. Diffuse aneurysmal disease (chronic aortic dissection, Marfan, and mega aorta syndromes) and multiple aneurysm. Ann Surg 1990;211:521-37.
23. [23] Pasic M, Segesser L, Carrel T, Laske A, Bauer E, Turina M. Surgical treatment of cardiovascular complications in Marfan syndrome: a 27-year experience. Eur J Cardio-thorac Surg 1992;6:149-55.
24. [24] Svensson LG, Crawford ES, Coselli JS, Safi HJ, Hess KR. Impact of cardiovascular operation on survival in the Marfan patient. Circulation 1989;80(Suppl. 1):I-233-42.
25. [25] Pyeritz RE. Marfan Syndrome: current and future clinical and genetic management of cardiovascular manifestations. Sem Thorac Cardiovasc Surg 1993;5:11-6.
26. [26] Haverich A, Miller DC, Scott WC. Acute and chronic aortic dissections: determinants of long-term outcome for operative survivors. Circulation 1985;72(2):II22-34.
27. [27] Crawford ES, Kirklin JW, Naftel DC, Svensson LG, Coselli JS, Safi HJ. Surgery for acute dissection of ascending aorta: should the arch be included? J Thorac Cardiovasc Surg 1992;104:46-59.
28. [28] Kirklin JW, Kouchoukos NT. When and how to include arch repair in patients with acute dissections involving the ascending aorta. Sem Thorac Cardiovasc Surg 1993;5:27-32.
29. [29] Marsele DL, Moodie DS, Vacante M, Lytle BW, Gill CC, Sterba R, Cosgrove DM, Passalacqua M, Goormastic M, Kovacs A. Marfan's Syndrome: natural history and long-term follow-up of cardiovascular involvement. J Am Coll Cardiol 1989;14:422-8.
30. [30] Kouchoukos NT, Marshall WG Jr., Wedige-Stecher TA. Eleven-year experience with composite graft replacement of the ascending aorta and aortic valve. J Thorac Cardiovasc Surg 1986;92:691-705.
31. [31] Crawford ES, Svensson LG, Coselli JS, Safi HJ, Hess KR. Surgical treatment of aneurysm and/or dissection of the ascending aorta, transverse aortic arch, and ascending aorta and transverse aortic arch. Factors influencing survival in 717 patients. J Thorac Cardiovasc Surg 1989;98:659-74.
32. [32] Heinemann MK, Laas J, Jurmann MJ, Karck M, Borst HG. Surgery extended into the aortic arch in acute type A aortic dissection: indications, techniques, results. Circulation 1991;84-Suppl. III:25-30.
33. [33] Laas J, Jurmann MJ, Heinemann MK, Borst HG. Advances in aortic arch surgery. Ann Thorac Surg 1992;53:227-32.
34. [34] Finkbohner R, Johnston D, Crawford ES, Coselli J, Milewicz DM. Marfan Syndrome. Long-term survival and complications after aortic aneurysm repair. Circulation 1995;91:728-33.
35. [35] Coselli JS, LeMaire SA, Büket S. Marfan Syndrome: the variability and outcome of operative management. J Vasc Surg 1995;21:432-43.
36. [36] Lehmann ED. Cardiovascular screening in Marfan's syndrome. Lancet 1995;345:1501.
37. [37] Miller DC, Mitchell RS, Oyer PE, Stinson EB, Jamieson SW, Shumway NE. Indipendent determinants of operative mortality for patients with aortic dissections. Circulation 1984;70:153-64.