Maple syrup urine disease: Nutritional management by intravenous hyperalimentation and uneventful course after surgical repair of dislocation of the hip

Journal of Inherited Metabolic Disease

Volumn 21, Issue 2, 1998, Pages 177-178

  Koga, Y ^a   Iwanaga, T ^a   Yoshida, I ^a   Yoshino, M ^a   Kaneko, S ^a   Kato, H ^a  

^a KURUME UNIVERSITY SCHOOL OF MEDICINE   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

BRANCHED CHAIN AMINO ACID;

ARTICLE; CASE REPORT; CLINICAL FEATURE; FEMALE; HIP DISLOCATION; HUMAN; KETOACIDOSIS; MAPLE SYRUP URINE DISEASE; PARENTERAL NUTRITION; SCHOOL CHILD;

CHILD; FEMALE; HIP DISLOCATION; HUMANS; MAPLE SYRUP URINE DISEASE; PARENTERAL NUTRITION, TOTAL;

EID: 0031980609     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1005324516186     Document Type: Article

References (2)

1. Berry GT, Heidenreich R, Kaplan P, et al (1991) Branched-chain amino acid-free parenteral nutrition in the treatment of acute metabolic decompensation in patients with maple syrup urine disease. N Engl J Med 324: 175-179.
2. Castellino P, Luzi L, Simonson DC, Haymond M, DeFronzo RA (1987) Effect of insulin and plasma amino acid concentrations on leucine metabolism in man. J Clin Invest 80: 1984-1993.