The molecular genetics of the long QT syndrome: Genes causing fainting and sudden death

Annual Review of Medicine

Volumn 49, Issue , 1998, Pages 263-274

  Vincent, G Michael ^a  

^a LDS HOSPITAL   (United States)

Author keywords

Genetics; Jervell; Lange Nielsen; QT interval; Romano Ward; Torsade de pointes

Indexed keywords

POTASSIUM CHANNEL; SODIUM CHANNEL;

ACTION POTENTIAL; AUTOSOMAL DOMINANT DISORDER; CHROMOSOME 4; EMOTIONAL STRESS; EXERCISE; GENE LOCUS; GENE MUTATION; HUMAN; LONG QT SYNDROME; MOLECULAR GENETICS; PENETRANCE; PHENOTYPE; PRIORITY JOURNAL; QT INTERVAL; REVIEW; SUDDEN DEATH; SYNCOPE; TORSADE DES POINTES;

ACTION POTENTIALS; ADULT; CATION TRANSPORT PROTEINS; CHILD; CHROMOSOME MAPPING; CHROMOSOMES, HUMAN, PAIR 4; DEATH, SUDDEN, CARDIAC; DIAGNOSIS, DIFFERENTIAL; DNA-BINDING PROTEINS; ELECTROCARDIOGRAPHY; EMOTIONS; ETHER-A-GO-GO POTASSIUM CHANNELS; EXERTION; GENE EXPRESSION; GENES, DOMINANT; GENOTYPE; HUMANS; KCNQ POTASSIUM CHANNELS; KCNQ1 POTASSIUM CHANNEL; LONG QT SYNDROME; MOLECULAR BIOLOGY; MUTATION; PHENOTYPE; POTASSIUM CHANNELS; POTASSIUM CHANNELS, VOLTAGE-GATED; SODIUM CHANNELS; SYNCOPE; TORSADES DE POINTES; TRANS-ACTIVATORS; VARIATION (GENETICS);

EID: 0031978985     PISSN: 00664219     EISSN: None     Source Type: Book Series    
DOI: 10.1146/annurev.med.49.1.263     Document Type: Review

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