Properdin deficiency: Rare presentation with meningococcal bone and joint infections

Pediatric Infectious Disease Journal

Volumn 17, Issue 4, 1998, Pages 356-358

  Rottem, Menachem ^a   Miron, Dan ^a   Shiloah, Elie ^a   Horovitz, Yoseph ^a   Schlezinger, Menachem ^a  

^a HAEMEK MEDICAL CENTER   (Israel)

Author keywords

[No Author keywords available]

Indexed keywords

CEFTRIAXONE; PROPERDIN;

ADOLESCENT; ADULT; ARTICLE; BACTERIAL ARTHRITIS; BONE INFECTION; CASE REPORT; COMPLEMENT DEFICIENCY; HUMAN; HUMAN CELL; HUMAN TISSUE; INFECTIOUS ARTHRITIS; MALE; NEISSERIA MENINGITIDIS; OSTEOMYELITIS; PRIORITY JOURNAL; PROPERDIN DEFICIENCY; PROTEIN DEFICIENCY;

ADOLESCENT; ARTHRITIS, INFECTIOUS; COMPLEMENT HEMOLYTIC ACTIVITY ASSAY; COMPLEMENT PATHWAY, ALTERNATIVE; COMPLEMENT PATHWAY, CLASSICAL; FEMALE; HUMANS; MALE; MENINGOCOCCAL INFECTIONS; NEISSERIA MENINGITIDIS; OSTEOMYELITIS; PEDIGREE; PROPERDIN;

EID: 0031970217     PISSN: 08913668     EISSN: None     Source Type: Journal    
DOI: 10.1097/00006454-199804000-00023     Document Type: Article

References (4)

1. Densen P, Weiler JM, Griffiss JM, Hoffmann LG. Familial properdin deficiency and fatal meningococcemia. N Engl J Med 1987;316:922-6.
2. Frank MM. Complement system. In: Frank MM, Austen KF, Claman HN, Unanue ER, eds. Samter's immunologic diseases. 5th ed. vol 1. ch 21. 1995:331-52.
3. Schlesinger M, Mashal U, Levy J, Fishelson Z. Hereditary properdin deficiency in three families of Tunisian Jews. Acta Paediatr 1993;82:744-7.
4. Derkx HH, Kuijper EJ, Fijen CA, Jak M, Dankert J, Van-Deventer SJ. Inherited complement deficiency in children surviving fulminant meningococcal septic shock. Eur J Pediatr 1995;154:735-8.