Cognitive functioning in adults with Williams syndrome

Journal of Child Psychology and Psychiatry and Allied Disciplines

Volumn 39, Issue 2, 1998, Pages 183-189

  Howlin, Patricia ^a   Davies, Mark ^a,b   Udwin, Orlee ^a,b,c  

^a ST GEORGE'S UNIVERSITY OF LONDON   (United Kingdom)

^b QUEEN'S UNIVERSITY BELFAST   (United Kingdom)

^c SOUTH LONDON AND MAUDSLEY NHS FOUNDATION TRUST   (United Kingdom)

Author keywords

Adulthood; Educational attainment; Intelligence; Natural history; Williams syndrome

Indexed keywords

ACADEMIC ACHIEVEMENT; ADULT; ARITHMETIC; ARTICLE; COGNITION; CONTROLLED STUDY; FEMALE; HUMAN; INTELLIGENCE; INTELLIGENCE QUOTIENT; LANGUAGE ABILITY; MAJOR CLINICAL STUDY; MALE; READING; SCORING SYSTEM; SOCIAL ADAPTATION; WILLIAMS BEUREN SYNDROME;

ADOLESCENT; ADULT; COGNITION; EDUCATIONAL STATUS; FEMALE; HUMANS; INTELLIGENCE; MALE; WILLIAMS SYNDROME;

EID: 0031951531     PISSN: 00219630     EISSN: None     Source Type: Journal    
DOI: 10.1017/S0021963097001789     Document Type: Article

References (44)

1. Arnold, R., Yule, W., & Martin, N. (1985). The psychological characteristics of Infantile Hypercalcaemia : A preliminary investigation. Development Medicine and Child Neurology, 27, 49-59.
2. Avery, R. O., Slate, J. R., & Chavan, W. (1989). A longitudinal study of WISC-R and WAIS-R scores with students who are educable mentally handicapped. Education and Training in Mental Retardation, 24, 28-31.
3. Bellugi, U., Wang, P. P., & Jernigan, T. L. (1994). Williams Syndrome: An unusual neuropsychological profile. In S. H. Broman & J. Grafman (Eds.), Atypical cognitive deficits in developmental disorders (pp. 23-56). Hillsdale, NJ: Lawrence Erlbaum.
4. Bennett, F. C., La Veck, B., & Sells, C. J. (1978). The Williams elphin faces syndrome; the psychological profile as an aid in syndrome identification. Pediatrics, 61, 303-306.
5. Carr, J. (1994). Long-term outcome for people with Down's syndrome. Journal of Child Psychology and Psychiatry, 35, 425-439.
6. Chapman, C. A., du Plessis, A., & Pober, B. R. (1996). Neurologic findings in adults and children with Williams syndrome. Journal of Child Neurology, 11, 63-65.
7. Crisco, J. J. (1990). Rate of cognitive development in young children with Williams syndrome. Clinical Research, 38, 536A.
8. Dilts, C.V., Morris, C. A., & Leonard, C. O. (1990). Hypothesis for development of the behavioral phenotype in Williams syndrome. American Journal of Medical Genetics, Supplement 6, 126-131.
9. Dunn, L. M., Dunn, L. M., Whetton, C., & Pintilie, D. (1982). The British Picture Vocabulary Scale. Windsor, U.K.: NFER-Nelson.
10. Dunst, C. J. (1988). Stage transitioning in the sensorimotor development of Down's syndrome infants. Journal of Mental Deficiency Research, 32, 405-410.
11. Dykens, E. M., Hodapp, R. M., Ort, S., Finucane, B., Shapiro, L. R., & Leckman, J. F. (1989). The trajectory of cognitive development in males with fragile X syndrome. Journal of the American Academy of Child and Adolescent Psychiatry, 28, 422-426.
12. Ewart, A. K., Morris, C. A., Atkinson, D., Jin, W., Sternes, K., Spallone, P., Stock, A. D., Leppert, M., & Keating, M. T. (1993). Hemizygosity at the elastin locus in a developmental disorder, Williams syndrome. Nature Genetics, 5, 11-16.
13. Gardner, M. F. (1982). Expressive One Word Vocabulary Test-Upper extension. Los Angeles, CA: Western Psychological Services.
14. Gardner, M. F. (1990). Expressive One Word Vocabulary Test-Revised. Los Angeles, CA: Western Psychological Services.
15. Gosch, A., & Pankau, R. (1994). Linguistic abilities in children with Williams-Beuren syndrome. American Journal of Medical Genetics, 52, 291-296.
16. Gosch, A., & Pankau, R. (1996). Longitudinal study of the cognitive development in children with Williams-Beuren syndrome. American Journal of Medical Genetics, 61, 26-29.
17. Hagerman, R. J., Schreiner, R. A., Kemper, M. B., Wittenberger, M. D., Zahn, B., & Habicht, K. (1989). Longitudinal IQ changes in fragile X males. American Journal of Mental Genetics, 33,513-518.
18. KarmilofT-Smith, A., Grant, J., Berthoud, L, Davies, M., Howlin, P., & Udwin, O. (1996). Language and Williams syndrome: How intact is "intact"? Child Development, 68, 274-290.
19. Kataria, S., Goldstein, D. J., & Kushnick, T. (1984). Developmental delays in Williams ("elphin faces") syndrome. Applied Research in Mental Retardation, 5, 419-423.
20. Lopez-Rangel, E., Maurice, M., McGillivray, B., & Friedman, J. M. (1992). Williams syndrome in adults. American Journal of Medical Genetics, 44, 720-729.
21. Martin, N. D. T., Snodgrass, G. J. A. I., & Cohen, R. D. (1984). Idiopathic Infantile Hypercalcaemia-a continuing enigma. Archives of Disease in Childhood, 59, 605-613.
22. Meyerson, M. D., & Frank, R. A. (1987). Annotation: Language, speech and hearing in Williams syndrome: Intervention approaches and research needs. Developmental Medicine and Child Neurology, 29, 258-262.
23. Morris, C. A., Demsey, S. A., Leonard, C. O., Dilts, C., & Blackburn, B. L. (1988). Natural history of Williams syndrome : Physical characteristics. The Journal of Pediatrics, 113, 318-326.
24. Morris, C. A., Leonard, C. O., Dilts, C., & Demsey, S. A. (1990). Adults with Williams syndrome. American Journal of Medical Genetics, Supplement 6, 102-107.
25. Pagon, R., Bennett, F., La Veck, B., Stewart, K., & Johnson, J. (1987). Williams syndrome: Features in late childhood and adolescence. Pediatrics, 18, 85-91.
26. Plissart, L., Borghraef, M., Volcke, P., Van der Berghe, H., & Fryns, J. P. (1994). Adults with Williams-Beuren syndrome: Evaluation of the medical, psychological and behavioural aspects. Clinical Genetics, 46, 161-167.
27. Pober, B. P., Lacro, V. L., Rice, C., Mandell, V., & Teele, R. L. (1993). Renal findings in 40 individuals with Williams syndrome. American Journal of Medical Genetics, 46, 271274.
28. Rubin, H. H., Goldman, J. J., & Rosenfeld, J. G. (1985). A comparison of WISC-R and WAIS-R IQs in a mentally retarded residential population. Psychology in the Schools, 22, 392-397.
29. Rutter, M., & Mawhood, L. (1991). Language delay: Longterm psychological sequelea. In M. Rutter&P. Casaer(Eds.), Biological risk factors for psychosocial disorders (pp. 233259). Cambridge: Cambridge University Press.
30. Sattler, J.( Polifka, S., & Hilsen, D. (1984). A longitudinal study of the WISC-R/WAIS-R score disparity with special education students. Psychology in the Schools, 21, 294-295.
31. Sparrow, S. S., Balla, D., & Cicchetti, D. (1984). Vineland Adaptive Behavior Scales. Circle Pines, MN: American Guidance Service.
32. Spitz, H. H. (1988). Inverse relationship between the WISCR/WAIS-R score disparity and IQ level in the lower range of intelligence. American Journal on Mental Retardation, 4, 376-378.
33. Udwin, O. (1990). A survey of adults with Williams syndrome and Idiopathic Infantile Hypercalcaemia. Developmental Medicine and Child Neurology, 32, 129-141.
34. Udwin, O., Davies, M., & Howlin, P. (1996). A longitudinal study of cognitive abilities and educational attainment in Williams Syndrome. Developmental Medicine and Child Neurology, 38, 1020-1029.
35. Udwin, O., & Yule, W. (1988). Infantile Hypercalcaemia and Williams syndrome: Guidelines for parents. Harlow, U.K.: Williams Syndrome Foundation.
36. Udwin, O., & Yule, W. (1990). Expressive language of children with Williams syndrome. American Journal of Medical Genetics, suppl 6, 109-114.
37. Udwin, O., & Yule, W. (1991). A cognitive and behavioural phenotype in Williams syndrome. Journal of Clinical ami Experimental Neuropsychology, 13, 232-244.
38. Udwin, O., Yule, W., & Martin, N. (1987). Cognitive abilities and behavioural characteristics of children with Idiopathic Infantile Hypercalcaemia. Journal of Child Psychology and Psychiatry, 28, 297-309.
39. Wechsler, D. (1976). Wechsler Intelligence Scale for Children-Revised (WISC-R). New York: The Psychological Corporation.
40. Wechsler, D. (1981). Wechsler Adult Intelligence ScaleRevised (WA1S-R). San Antonio, TX: The Psychological Corporation.
41. Wechsler, D. (1986). Wechsler Adult Intelligence Scale-Revised U.K. Edition ( WAIS-R UK). Sidcup, U.K. : The Psychological Corporation.
42. Wechsler, D. (1992). Wechsler Intelligence Scale for ChildrenThird UK Edition (WISC-III UK). Sidcup, U.K.: The Psychological Corporation.
43. Wechsler, D. (1993). Wechsler Objective Reading Dimensions (WORD). Sidcup, U.K.: The Psychological Corporation.
44. World Health Organization (1992). International classification of disorders, 10th revision (ICD-10): Classification of mental and behavioural disorders. Clinical description and diagnostic guidelines. Geneva: Author.