Hereditary cholestasis with lymphoedema (Aagenaes syndrome, cholestasis- lymphoedema syndrome): New cases and follow-up from infancy to adult age

Scandinavian Journal of Gastroenterology

Volumn 33, Issue 4, 1998, Pages 335-345

  Aagenaes, Øystein ^a  

^a AKER UNIVERSITY HOSPITAL   (Norway)

Author keywords

[No Author keywords available]

Indexed keywords

ALANINE AMINOTRANSFERASE; ALKALINE PHOSPHATASE; ALPHA TOCOPHEROL; ASCORBIC ACID; BILE ACID; BILIRUBIN; COLESTYRAMINE; GAMMA GLUTAMYLTRANSFERASE; MEDIUM CHAIN TRIACYLGLYCEROL; PHENOBARBITAL; RETINOL; VITAMIN; VITAMIN B GROUP; VITAMIN D; VITAMIN K GROUP;

ADOLESCENT; ADULT; CHILD; CHOLESTASIS; CLINICAL ARTICLE; FEMALE; FOLLOW UP; GENETIC DISORDER; HISTOPATHOLOGY; HUMAN; LIVER CIRRHOSIS; LYMPHEDEMA; MALE; NORWAY; PEDIGREE ANALYSIS; PRIORITY JOURNAL; REVIEW;

ADOLESCENT; ADULT; CHILD; CHILD, PRESCHOOL; CHOLESTASIS; CONSANGUINITY; FEMALE; FOLLOW-UP STUDIES; GENES, RECESSIVE; HUMANS; INFANT; LIVER CIRRHOSIS; LIVER FUNCTION TESTS; LYMPHEDEMA; MALE; MIDDLE AGED; MINNESOTA; NORWAY; PEDIGREE; PHENOBARBITAL; PREGNANCY; SYNDROME; TIME FACTORS;

EID: 0031948707     PISSN: 00365521     EISSN: None     Source Type: Journal    
DOI: 10.1080/00365529850170955     Document Type: Review

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