Cerebellar neurodegeneration in human hereditary DNA repair disorders

Neuroscience Letters

Volumn 243, Issue 1-3, 1998, Pages 133-136

  Kohji, Toshihiko ^a,b   Hayashi, Masaharu ^a   Shioda, Kei ^c   Minagawa, Masao ^c   Morimatsu, Yoshio ^a   Tamagawa, Kimiko ^d   Oda, Masaya ^d  

^a Tokyo Metropolitan Institute   (Japan)

^b TOKYO MEDICAL AND DENTAL UNIVERSITY   (Japan)

^c SAITAMA MEDICAL UNIVERSITY   (Japan)

^d TOKYO METROPOLITAN NEUROLOGICAL HOSPITAL   (Japan)

Author keywords

Apoptosis; Bax; Cerebellum; Cockayne syndrome; Granule cells; P53; TdT mediated DIG dUTP nick end labeling; Trk B; Xeroderma pigmentosum

Indexed keywords

PROTEIN BAX; PROTEIN P53;

ADOLESCENT; ADULT; APOPTOSIS; ARTICLE; CEREBELLUM CORTEX; CEREBELLUM DEGENERATION; CHILD; CLINICAL ARTICLE; COCKAYNE SYNDROME; DNA REPAIR; FEMALE; GRANULE CELL; HUMAN; IMMUNOHISTOCHEMISTRY; MALE; NEUROPATHOLOGY; PRIORITY JOURNAL; PROTEIN EXPRESSION; XERODERMA PIGMENTOSUM;

ADOLESCENT; ADULT; BCL-2-ASSOCIATED X PROTEIN; BIOTIN; BRAIN CHEMISTRY; CEREBELLAR DISEASES; CHILD; COCKAYNE SYNDROME; DEOXYURACIL NUCLEOTIDES; DNA FRAGMENTATION; DNA REPAIR; FEMALE; HUMANS; MALE; NERVE DEGENERATION; NEUROPROTECTIVE AGENTS; PROTO-ONCOGENE PROTEINS; PROTO-ONCOGENE PROTEINS C-BCL-2; RECEPTOR PROTEIN-TYROSINE KINASES; RECEPTOR, CILIARY NEUROTROPHIC FACTOR; RECEPTORS, NERVE GROWTH FACTOR; STAINING AND LABELING; TUMOR SUPPRESSOR PROTEIN P53; XERODERMA PIGMENTOSUM;

EID: 0031932262     PISSN: 03043940     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0304-3940(98)00109-8     Document Type: Article

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