Down-regulation of cholesterol biosynthesis in sitosterolemia: Diminished activities of acetoacetyl-COa thiolase, 3-hydroxy-3- methylglutaryl-COa synthase, reductase, squalene synthase, and 7- dehydrocholesterol δ7-reductase in liver and mononuclear leukocytes

Journal of Lipid Research

Volumn 39, Issue 1, 1998, Pages 44-50

  Honda, Akira ^a   Salen, Gerald ^a   Nguyen, Lien B ^a   Tint, G Stephen ^a   Batta, Ashok K ^a   Shefer, Sarah ^a  

^a NONE

Author keywords

LDL receptor; Sitosterol

Indexed keywords

ACETYL COENZYME A ACETYLTRANSFERASE; HYDROXYMETHYLGLUTARYL COENZYME A REDUCTASE; HYDROXYMETHYLGLUTARYL COENZYME A SYNTHASE; SITOSTEROL; SQUALENE SYNTHASE;

ADULT; ARTICLE; CASE REPORT; CHOLESTEROL SYNTHESIS; DOWN REGULATION; ENZYME ACTIVITY; ENZYME REGULATION; FEMALE; HUMAN; HYPERCHOLESTEROLEMIA; PATHOPHYSIOLOGY; PRIORITY JOURNAL; RECESSIVE INHERITANCE;

ACETYL-COA C-ACETYLTRANSFERASE; ADULT; CHOLESTEROL; FARNESYL-DIPHOSPHATE FARNESYLTRANSFERASE; HUMANS; HYDROXYMETHYLGLUTARYL COA REDUCTASES; HYDROXYMETHYLGLUTARYL-COA SYNTHASE; LEUKOCYTES, MONONUCLEAR; LIVER; MALE; OXIDOREDUCTASES; OXIDOREDUCTASES ACTING ON CH-CH GROUP DONORS; SITOSTEROLS;

EID: 0031906443     PISSN: 00222275     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

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