Recombinant human acid α-glucosidase corrects acid α-glucosidase- deficient human fibroblasts, quail fibroblasts, and quail myoblasts

Pediatric Research

Volumn 43, Issue 3, 1998, Pages 374-380

  Yang, Helen Wen ^a   Kikuchi, Tateki ^b   Hagiwara, Yasuko ^b   Mizutani, Makoto ^c   Chen, Yuan Tsong ^a   Van Hove, Johan L K ^a  

^a DUKE UNIVERSITY MEDICAL CENTER   (United States)

^b NATIONAL INSTITUTE OF NEUROSCIENCE   (Japan)

^c NIPPON INSTITUTE FOR BIOLOGICAL SCIENCE   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

GLUCAN 1,4 ALPHA GLUCOSIDASE; GLYCOGEN; MANNOSE 6 PHOSPHATE; RECOMBINANT GLUCAN 1,4 ALPHA GLUCOSIDASE; RECOMBINANT PROTEIN; SOMATOMEDIN B RECEPTOR; UNCLASSIFIED DRUG;

ANIMAL CELL; ARTICLE; CONTROLLED STUDY; DRUG MEGADOSE; ENDOCYTOSIS; ENZYME REPLACEMENT; FIBROBLAST; GLYCOGEN STORAGE DISEASE TYPE 2; HUMAN; HUMAN CELL; MYOBLAST; NONHUMAN; PRIORITY JOURNAL; QUAIL;

EID: 0031886065     PISSN: 00313998     EISSN: None     Source Type: Journal    
DOI: 10.1203/00006450-199803000-00011     Document Type: Article

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