Pathological study of mice with total deficiency of sphingolipid activator proteins (SAP knockout mice)

Acta Neuropathologica

Volumn 96, Issue 1, 1998, Pages 29-40

  Oya, Yasushi ^a   Nakayasu, Hiroyuki ^a   Fujita, Nobuya ^a   Suzuki, Kunihiko ^a   Suzuki, Kinuko ^a  

^a UNIVERSITY OF NORTH CAROLINA SCHOOL OF MEDICINE   (United States)

Author keywords

Axonal spheroid; Knockout mouse; Lysosomal storage disease; Phosphorylated neurofilaments; Sphingolipid activator protein (saposin)

Indexed keywords

ANTIBODY; PROTEIN PRECURSOR; SPHINGOLIPID ACTIVATOR PROTEIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; ASTROCYTOSIS; CENTRAL NERVOUS SYSTEM; CHOROID PLEXUS; CONTROLLED STUDY; DENDRITE; ENDOTHELIUM CELL; EPITHELIUM CELL; FIBROBLAST; GAUCHER DISEASE; GENE DISRUPTION; GLIA CELL; KNOCKOUT MOUSE; LAMELLAR BODY; LIVER; LYSOSOME STORAGE DISEASE; MACROPHAGE; METACHROMATIC LEUKODYSTROPHY; MOUSE; MUSCLE; NERVE CELL; NERVE FIBER; NEUROFILAMENT; NEUROLOGIC DISEASE; NONHUMAN; PERIKARYON; PERIPHERAL NERVE; PRIORITY JOURNAL; PROTEIN DEFICIENCY; SCHWANN CELL; SKIN; SPINAL GANGLION; TUMOR SPHEROID; ULTRASTRUCTURE; VASCULAR ENDOTHELIUM;

ANIMALS; AXONS; BRAIN; GLYCOPROTEINS; HUMANS; MICE; MICE, KNOCKOUT; MICROSCOPY, ELECTRON; MUSCLE, SKELETAL; NERVOUS SYSTEM; NEUROGLIA; NEURONS; PERIPHERAL NERVES; PHENOTYPE; SAPOSINS; SPHEROIDS, CELLULAR; SPHINGOLIPID ACTIVATOR PROTEINS; TIME FACTORS;

EID: 0031804903     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s004010050857     Document Type: Article

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