Evidence for furin-type activity-mediated C-terminal processing of profibrillin-1 and interference in the processing by certain mutations

Human Molecular Genetics

Volumn 7, Issue 13, 1998, Pages 2039-2044

  Lonnqvist L ^a   Reinhardt, D ^b   Sakai, L ^b   Peltonen, L ^a  

^a NATIONAL PUBLIC HEALTH INSTITUTE   (Finland)

^b OREGON HEALTH AND SCIENCE UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

FIBRILLIN; FURIN; PROTEIN PRECURSOR; RECOMBINANT PROTEIN;

AMINO TERMINAL SEQUENCE; ANIMAL CELL; ARTICLE; CARBOXY TERMINAL SEQUENCE; CONTROLLED STUDY; ENZYME ACTIVITY; GENE MUTATION; NONHUMAN; PRIORITY JOURNAL; PROTEIN PROCESSING; SITE DIRECTED MUTAGENESIS;

EID: 0031789366     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/7.13.2039     Document Type: Article

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