Corrective gene transfer of keratinocytes from patients with junctional epidermolysis bullosa restores assembly of hemidesmosomes in reconstructed epithelia

Gene Therapy

Volumn 5, Issue 10, 1998, Pages 1322-1332

  Vailly, J ^a   Gagnoux Palacios, L ^a   Dell'Ambra, E ^b   Romero C ^a   Pinola, M ^b   Zambruno, G ^b   De Luca, M ^b   Ortonne, J P ^a,c   Meneguzzi, G ^a  

^a INSERM   (France)

^b LABORATORIO DI PATOLOGIA VASCOLARE   (Italy)

^c CENTRE HOSPITALIER UNIVERSITAIRE DE NICE   (France)

Author keywords

Artificial epidermis; Basement membrane; Cell adhesion; Extracellular matrix; Laminin 5

Indexed keywords

LAMININ; RECOMBINANT PROTEIN;

ARTICLE; BASEMENT MEMBRANE; CASE REPORT; CELL ADHESION; CELL SPREADING; CONTROLLED STUDY; EPIDERMOLYSIS BULLOSA; EPITHELIUM; EXTRACELLULAR MATRIX; GENE TRANSFER; HEMIDESMOSOME; HUMAN; HUMAN CELL; INTERMEDIATE FILAMENT; KERATINOCYTE; NUCLEOTIDE SEQUENCE; ORGAN CULTURE; PRIORITY JOURNAL; PROTEIN SECRETION; TRANSGENE;

EID: 0031787239     PISSN: 09697128     EISSN: None     Source Type: Journal    
DOI: 10.1038/sj.gt.3300730     Document Type: Article

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