Expression analysis of two mutant human ornithine transcarbamylases in COS-7 cells

Journal of Human Genetics

Volumn 43, Issue 1, 1998, Pages 54-58

  Kogo, Toshiaki ^b   Satoh, Yoshinori ^b   Kanazawa, Masaki ^a   Yamamoto, Shigenori ^a   Takayanagi, Masaki ^c   Ohtake, Akira ^d   Mori, Masataka ^e   Niimi, Hiroo ^a  

^a CHIBA UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^b SHIMOSHIZU HOSPITAL   (Japan)

^c CHIBA CHILDREN'S HOSPITAL   (Japan)

^d SAITAMA MEDICAL UNIVERSITY   (Japan)

^e KUMAMOTO UNIV SCHOOL OF MEDICINE   (Japan)

Author keywords

COS 7 cells; Mitochondrial import; Ornithine transcarbamylase deficiency; Processing; Pulse and pulse chase experiments

Indexed keywords

ORNITHINE CARBAMOYLTRANSFERASE;

ANIMAL CELL; ARTICLE; CONTROLLED STUDY; DIAGNOSTIC VALUE; ENZYME ANALYSIS; ENZYME LOCALIZATION; HYPERAMMONEMIA; LIVER MITOCHONDRION; NONHUMAN; UREA CYCLE; X CHROMOSOMAL INHERITANCE;

ANIMALIA;

EID: 0031776370     PISSN: 14345161     EISSN: None     Source Type: Journal    
DOI: 10.1007/s100380050037     Document Type: Article

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