Alterations in the biosynthesis of cholesterol, dolichol and dolichyl-P in the genetic cholesterol homeostasis disorder, Niemann-Pick type C disease

Biochimica et Biophysica Acta - Lipids and Lipid Metabolism

Volumn 1394, Issue 2-3, 1998, Pages 177-186

  Schedin, Sophia ^a   Nilsson, Maria ^a   Chojnacki, Tadeusz ^b   Dallner, Gustav ^a  

^a STOCKHOLM UNIVERSITY   (Sweden)

^b INSTITUTE OF BIOCHEMISTRY AND BIOPHYSICS   (Poland)

Author keywords

3H Mevalonate; cis Prenyltransferase; Intracellular cholesterol transport; Niemann Pick type C disease; Squalene synthase

Indexed keywords

CHOLESTEROL; DIMETHYLALLYLTRANSFERASE; DOLICHOL; DOLICHOL PHOSPHATE; HYDROXYMETHYLGLUTARYL COENZYME A REDUCTASE; MEVALONIC ACID; SQUALENE; SQUALENE SYNTHASE; TRITIUM;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BRAIN HOMOGENATE; CHOLESTEROL LIVER LEVEL; CHOLESTEROL SYNTHESIS; CONTROLLED STUDY; ENZYME ACTIVITY; ISOTOPE LABELING; LIVER HOMOGENATE; LIVER MICROSOME METABOLISM; MALE; MOUSE; NIEMANN PICK DISEASE; NONHUMAN; PRIORITY JOURNAL;

ANIMALS; BRAIN; CHOLESTEROL; DISEASE MODELS, ANIMAL; DOLICHOL; DOLICHOL PHOSPHATES; FARNESYL-DIPHOSPHATE FARNESYLTRANSFERASE; HYDROXYMETHYLGLUTARYL COA REDUCTASES; LIVER; MALE; MEVALONIC ACID; MICE; MICE, INBRED BALB C; MICROSOMES, LIVER; NIEMANN-PICK DISEASES; SQUALENE; TRANSFERASES; TRITIUM;

MURINAE;

EID: 0031761031     PISSN: 00052760     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0005-2760(98)00108-8     Document Type: Article

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