A case report of steroid-responsive progressive encephalomyelitis with rigidity showing muscle stiffness limited to the upper body

Clinical Neurology

Volumn 38, Issue 7, 1998, Pages 680-682

  Matsuno, Sayoko ^a   Ohkoshi, Norio ^a   Hayashi, Akito ^a   Ishii, Akiko ^a   Shoji, Shin'ichi ^a  

^a UNIVERSITY OF TSUKUBA   (Japan)

Author keywords

Adrenocortical hormone therapy; Antinuclear antibody; Encephalomyelitis; Muscle stiffness; Progressive encephalomyelitis with rigidity; Stiff man syndrome

Indexed keywords

ANTINUCLEAR ANTIBODY; CORTICOSTEROID; METHYLPREDNISOLONE; PREDNISOLONE;

ADULT; ARTICLE; AUTOIMMUNE DISEASE; CASE REPORT; CEREBROSPINAL FLUID ANALYSIS; CLINICAL FEATURE; ELECTROENCEPHALOGRAM; ELECTROMYOGRAM; ENCEPHALOMYELITIS; FEMALE; HORMONAL THERAPY; HUMAN; MUSCLE SPASM; MUSCLE STIFFNESS; NUCLEAR MAGNETIC RESONANCE IMAGING; PLEOCYTOSIS; STIFF MAN SYNDROME;

ADMINISTRATION, ORAL; ADULT; AUTOIMMUNE DISEASES; ENCEPHALOMYELITIS; FEMALE; GLUCOCORTICOIDS; HUMANS; METHYLPREDNISOLONE; MUSCLE RIGIDITY; PREDNISOLONE;

EID: 0031741936     PISSN: 0009918X     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

References (10)

1. Whiteley AM, Swash M, Urich H : Progressive encephalomyelitis with rigidity : its relation to 'subacute myoclonic spinal neuronitis' and to the 'stiff-man syndrome'. Brain 99 : 27-42, 1976
2. Howell DA, Lees AJ, Toghill PJ : Spinal internuncial neurones in progressive encephalomyelitis with rigidity J Neurol Neurosurg Psychiatry 42 : 773-785, 1979
3. McCombe PA, Chalk JB, Searle JW, et al : Progressive encephalomyelitis with rigidity : a case report with magnetic resonance imaging findings. J Neurol Neurosurg Psychiatry 52 : 1429-1431, 1989
4. Burn DJ, Ball J, Lees AJ, et al : A case of progressive encephalomyelitis with rigidity and positive antiglutamic acid dehydrogenase antibodies. J Neurol Neurosurg Psychiatry 54 : 449-451, 1991
5. Kasperk S, Zebrowski S : Stiff-man syndrome and encehalomyelitis : report of a case. Arch Neurol 24 : 22-30, 1971
6. Casado JL, Gil-Perelta A, Graus F, et al : Anti-Ri antibodies associated with opsoclonus and progressive encephalomyelitis with rigidity. Neurology 44 : 1521-1522, 1994
7. Bolay H, Soylemezoglu F, Nurlu G, et al : PCR detected hepatitis C virus genome in the brain of a case with progressive encephalomyelitis with rigidity. Clin Neurol Neurosurg. 98 : 305-308, 1996
8. Fogan L : Progressive encephalomyelitis with rigidity responsive to plasmapheresis and immunosuppression. Ann Neurol 40 : 451-453, 1996