Primary pulmonary hypertension in childhood

Archives of Disease in Childhood

Volumn 79, Issue 5, 1998, Pages 452-455

  Haworth, Sheila G ^a  

^a KING'S COLLEGE LONDON   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

ACETYLCHOLINE; ACETYLSALICYLIC ACID; ADENOSINE; CALCIUM CHANNEL BLOCKING AGENT; DIPYRIDAMOLE; NITRIC OXIDE; PROSTACYCLIN; VASODILATOR AGENT; WARFARIN;

AUTOIMMUNE DISEASE; CHILD; CHROMOSOME 2Q; CLINICAL FEATURE; GENETIC PREDISPOSITION; HLA SYSTEM; HUMAN; PATHOGENESIS; PRIORITY JOURNAL; PULMONARY HYPERTENSION; REVIEW; TREATMENT PLANNING;

EID: 0031732093     PISSN: 00039888     EISSN: 14682044     Source Type: Journal    
DOI: 10.1136/adc.79.5.452     Document Type: Review

References (33)

1. The International Primary Pulmonary Hypertension Study Group. The international primary pulmonary hypertension study (IPPHS). Chest 1994;105:37S-41S.
2. Barst RJ, Long W, Gersony W. Long-term vasodilator treatment improves survival in children with primary pulmonary hypertension. Cardiology in the Young 1993;3:89.
3. Barst RJ. Primary pulmonary hypertension in children. In: Rubin LJ, Rich S, eds. Primary pulmonary hypertension. New York: Marcel Dekker, 1987:179-225.
4. Rich S, Dantzker DR, Ayres SM. Primary pulmonary hypertension: a national prospective study. Ann Intern Med 1987;107:216-23.
5. Langleben D. Familial primary pulmonary hypertension. Chest 1994;105:13S-16S.
6. Loyd JE, Primm, RK, Newman JH. Familial primary pulmonary hypertension: clinical patterns. Am Rev Respir Dis 1984;129:194-7.
7. Loyd JE, Butler MG, Foroud TM, Conneally PM, Phillips JAI, Newman JH. Genetic anticipation and abnormal gender ratio at birth in familial primary pulmonary hypertension. Am J Respir Crit Care Med 1995;152:93-7.
8. Nichols WC, Koller DL, Slovis B, et al. Localization of the gene for familial primary pulmonary hypertension to chromosome 2q31-32. Nat Genet 1997;15:277-80.
9. Gurtner HP. Aminorex and pulmonary hypertension. Cor Vasa 1985;27:160-71.
10. Mark EJ, Patalas ED, Chang HT, Evans RJ, Kessler SC. Fatal pulmonary hypertension associated with short-term use of fenfluramine and phentermine. N Engl J Med 1998; 337:602-6.
11. Polos PG, Wolfe D, Harley RA. Pulmonary hypertension and human immuno-deficiency virus infection: two reports and a review of the literature. Chest 1992;101:474-8.
12. Asherson RA, Higenbottam TW, Dinh Xuan AT, Khamashta MA, Hughes GRV. Pulmonary hypertension in a lupus clinic: experience with twenty-four patients. J Rheumatol 1990;17:1292-8.
13. Barst RJ, Flaster ER, Menon A, Fotino M, Morse JH. Evidence for the association of unexplained pulmonary hypertension in children with the major histocompatibility complex. Circulation 1992;85:249-58.
14. Weir EK, Reeve HL, Huang JM, et al. Anorexic agents aminorex, fenfluramine, and dexfenfluramine inhibit potassium current in rat pulmonary vascular smooth muscle and cause pulmonary vasoconstriction. Circulation 1996;94: 2216-20.
15. Riley MS, Porszasz J, Miranda J, Engelen MP, Brundage B, Wasserman K. Exhaled nitric oxide during exercise in primary pulmonary hypertension and pulmonary fibrosis. Chest 1997;111:44-50.
16. Stewart DJ, Levy RD, Cernacek P, Langleben D. Increased plasma endothelin-1 in pulmonary hypertension: marker or mediator of disease? Ann Intern Med 1991;114:464-9.
17. Christman BW, McPherson CD, Newman JH, et al. An imbalance between the excretion of thromboxane and prostacyclin metabolites in pulmonary hypertension. N Eng J Med 1992;327:70-5.
18. Eisenberg PR, Lucore C, Kaufmann E. Fibrinopeptide A levels indicative of pulmonary vascular thrombosis in patients with primary pulmonary hypertension. Circulation 1990;82:841-7.
19. Herve P, Launay JM, Scrobohaci ML, et al. Increased plasma serotonin in primary pulmonary hypertension. Am J Med 1995;99:249-54.
20. Fuster V, Steele PM, Edwards WP, Gersh BJ, McGoon MD, Frye RL. Primary pulmonary hypertension: natural history and the importance of thrombosis. Circulation 1984;70:580-7.
21. Mikkilineni S, Barst RJ, Cropp GJ. Pulmonary function in primary pulmonary hypertension. Pediatr Res 1990;27: 359A.
22. Rhodes J, Barst RJ, Garofano RP, Thoele DG, Gersony WM. Hemodynamic correlates of exercise function in patients with primary pulmonary hypertension. J Am Coll Cardiol 1991;18:1738-44.
23. Morse JH, Barst RJ, Fotino M. Familial pulmonary hypertension: immunogenetic findings in four Caucasian kindreds. Am Rev Respir Dis 1992;145:787-92.
24. Polos PG, Wolfe D, Harley RA, Strange C, Sahn SA. Pulmonary hypertension and human immunodeficiency virus infection. Chest 1992;101:474-8.
25. D'Angelo A, Della Valle P, Crippa L, Pattarini E, Grimaldi LMG, D'Angelo SV. Autoimmune protein S deficiency in a boy with severe thromboembolic disease. N Engl J Med 1993;328:1753-7.
26. Bowyer JJ, Busst CM, Denison DM, Shinebourne EA. Effect of long term oxygen treatment at home in children with pulmonary vascular disease. Br Heart J 1986;55:385-90.
27. Barst RJ. Treatment of primary pulmonary hypertension with continuous intravenous prostacyclin. Heart 1997;77: 299-301.
28. McLaughlin VV, Genthner DE, Panella MM, Rich S. Reduction in pulmonary vascular resistance with long-term epoprostenol (prostacyclin) therapy in primary pulmonary hypertension. N Engl J Med 1998;338:273-7.
29. Barst RJ, Rubin LJ, Long WA, Goon MD, Rich S, Badesch DB. A comparison of continuous intravenous epoprostenol (prostacyclin) with conventional treatment for primary pulmonary hypertension. N Engl J Med 1996;334:296-301.
30. Barst RJ. Pharmacologically induced pulmonary vasodilatation in children and young adults with primary pulmonary hypertension. Chest 1986;98:497-503.
31. Barst RJ, Rubin LJ, McGoon MD, Caldwell EJ, Long WA, Levy PS. Survival in primary pulmonary hypertension with long-term continuous intravenous prostacyclin. Ann Intern Med 1994;121:409-15.
32. Jones DA, Benjamin CW, Linseman DA. Activation of thromboxane and prostacyclin receptors elicits opposing effects on vascular smooth muscle cell growth and mitogen-activated protein kinase signaling cascades. Mol Pharmacol 1995;48:890-6.
33. Kerstein D, Levy PS, Hsu DT, Hordof AJ, Gersony WM, Barst RJ. Blade balloon atrial septostomy in patients with severe primary pulmonary hypertension. Circulation 1995; 91:2028-35.