Glycogen storage diseases and the liver

Bailliere's Clinical Gastroenterology

Volumn 12, Issue 2, 1998, Pages 337-354

  Burchell, Ann ^a  

^a UNIVERSITY OF DUNDEE   (United Kingdom)

Author keywords

Branching enzyme; Debranching enzyme; Glucose 6 phosphatase; Glycogen storage disease; Glycogen synthase; Hypoglycaemia; Liver; Phosphorylase; Phosphorylase kinase

Indexed keywords

ADULT; CARBOHYDRATE METABOLISM; CHILD; CLINICAL FEATURE; DIET THERAPY; GLUCOSE BLOOD LEVEL; GLUCOSE HOMEOSTASIS; GLYCOGEN METABOLISM; GLYCOGEN STORAGE DISEASE TYPE 1; GLYCOGEN STORAGE DISEASE TYPE 3; GLYCOGEN STORAGE DISEASE TYPE 4; GLYCOGEN STORAGE DISEASE TYPE 6; HEPATOMEGALY; HUMAN; HYPOGLYCEMIA; INFANT; LIVER; METABOLIC REGULATION; MOLECULAR BIOLOGY; PRIORITY JOURNAL; QUALITY OF LIFE; REVIEW;

EID: 0031654639     PISSN: 09503528     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0950-3528(98)90138-5     Document Type: Article

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