Accumulation of cholesterol and G(M2) ganglioside in cells cultured in the presence of progesterone: An implication for the basic defect in Niemann-Pick disease type C

Brain and Development

Volumn 20, Issue 1, 1998, Pages 50-52

  Sato, Masahiro ^a   Akaboshi, Shinjiro ^a   Katsumoto, Tetsuo ^a   Taniguchi, Miyako ^a   Higaki, Katsumi ^a   Tai, Tadashi ^b   Sakuraba, Hitoshi ^b   Ohno, Kousaku ^a  

^a TOTTORI UNIVERSITY   (Japan)

^b Immunol Clin Genet Tokyo M   (Japan)

Author keywords

Cholesterol; G(M2) ganglioside; Inhibitor; Intracellular transport; Progesterone

Indexed keywords

1 [N,O BIS(5 ISOQUINOLINESULFONYL) N METHYLTYROSYL] 4 PHENYLPIPERAZINE; CHOLESTEROL; GANGLIOSIDE GM2; IMIPRAMINE; PROGESTERONE; 1 (5 ISOQUINOLINESULFONYL) 2 METHYLPIPERAZINE; DRUG DERIVATIVE;

ANIMAL CELL; ARTICLE; FIBROBLAST CULTURE; HUMAN; HUMAN CELL; INTRACELLULAR TRANSPORT; NIEMANN PICK DISEASE; NONHUMAN; RAT; ANIMAL; CELL CULTURE; CLASSIFICATION; DRUG EFFECT; FIBROBLAST; FLUORESCENT ANTIBODY TECHNIQUE; METABOLISM; PATHOLOGY; TRANSPORT AT THE CELLULAR LEVEL;

1-(5-ISOQUINOLINESULFONYL)-2-METHYLPIPERAZINE; ANIMALS; BIOLOGICAL TRANSPORT; CELLS, CULTURED; CHOLESTEROL; FIBROBLASTS; FLUORESCENT ANTIBODY TECHNIQUE; G(M2) GANGLIOSIDE; HUMANS; IMIPRAMINE; NIEMANN-PICK DISEASES; PROGESTERONE; RATS;

EID: 0031594702     PISSN: 03877604     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0387-7604(97)00099-5     Document Type: Article

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