Turnover of F1F0-ATP synthase subunit 9 and other proteolipids in normal and Batten disease fibroblasts

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1361, Issue 3, 1997, Pages 251-262

  Tanner, Allison ^a   Shen, Bing Hua ^a   Fred Dice, J ^a  

^a TUFTS UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

Batten's disease; Degenerative disease; F0F1 ATPase; Fibroblast; Lysosomal storage disease; Mitochondria

Indexed keywords

PROTEOLIPID; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATE SYNTHASE; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATASE;

ARTICLE; DEGENERATIVE DISEASE; ENZYME METABOLISM; ENZYME SUBUNIT; FIBROBLAST; HUMAN; HUMAN CELL; LYSOSOME STORAGE DISEASE; MALE; MITOCHONDRION; NEURONAL CEROID LIPOFUSCINOSIS; PRIORITY JOURNAL; ANIMAL; BIOSYNTHESIS; C57BL MOUSE; CHEMISTRY; ENZYMOLOGY; KINETICS; METABOLISM; MOUSE; PATHOLOGY;

ANIMALS; FIBROBLASTS; HUMANS; KINETICS; MICE; MICE, INBRED C57BL; NEURONAL CEROID-LIPOFUSCINOSES; PROTEOLIPIDS; PROTON-TRANSLOCATING ATPASES;

EID: 0031585398     PISSN: 09254439     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0925-4439(97)00048-3     Document Type: Article

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