Sickle-cell disease

Lancet

Volumn 350, Issue 9079, 1997, Pages 725-730

  Serjeant, Graham R ^a  

^a UNIVERSITY OF THE WEST INDIES   (Jamaica)

Author keywords

[No Author keywords available]

Indexed keywords

GENETICS; HOSPITALIZATION; HUMAN; PATHOPHYSIOLOGY; REVIEW; SICKLE CELL ANEMIA;

ANEMIA, SICKLE CELL; HUMANS; SEVERITY OF ILLNESS INDEX;

EID: 0031556258     PISSN: 01406736     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0140-6736(97)07330-3     Document Type: Review

References (34)

1. Chebloune Y, Pagnier J, Trabuchet G, et al. Structural analysis of the 5' flanking region of the β-globin gene in African sickle cell anemia patients: further evidence for three origins of the sickle cell mutation in Africa. Proc Natl Acad Sci USA 1988; 85: 4431-35.
2. Kulozik AE, Wainscoat JS, Serjeant GR, et al. Geographical survey of βs-globin gene haplotypes: evidence for an independent Asian origin of the sickle-cell; mutation. Am J Hum Genet 1986; 39: 239-44.
3. Lopez R, Shimizu N, Cooperman JM. Recurrent folic acid deficiency in sickle cell disease. Am J Dis Child 1973; 125: 544-48.
4. Serjeant GR, Topley JM, Mason K, et al. Outbreak of aplastic crises in sickle cell anaemia associated with parvovirus-like agent Lancet 1981; ii: 595-97.
5. Webb DKH, Darby JS, Dunn DT, Terry SI, Serjeant GR. Gallstones in Jamaican children wtih homozygous sickle cell disease. Arch Dis Child 1989; 64: 693-96.
6. John AB, Ramial A, Jackson H, Maude GH, Waight-Sharma A, Serjeant GR. Prevention of pneumococcal infection in children with homozygous sickle cell disease. BMJ 1984; 288: 1567-70.
7. Gaston MH, Verter Ji, Woods G, et al. Prophylaxis with oral penicillin in children with sickle cell anemia. N Engl J Med 1986; 314: 1593-99.
8. Emond AM, Collis R, Darvill D, Higgs DR, Maude GH, Serjeant GR. Acute splenic sequestration in homozygous sickle cell disease: natural history and management. J Pediatr 1985; 107: 201-06.
9. Singhal A, Thomas PW, Keatney T, Venugopal S, Serjeant GR. Acceleration in linear growth after splenectomy for hypersplenism in homozygous sickle cell disease. Arch Dis Child 1995; 72: 227-29.
10. Balkaran B, Char G, Morris JS, Serjeant BE, Serjeant GR. Stroke in a cohort study of patients with homozygous sickle cell disease. J Pediatr 1992; 120: 360-66.
11. Powars D, Wilson B, Imbus C, Pegelow C, Allen J. The natural history of stroke in sickle cell disease. Am J Med 1978; 65: 461-71.
12. Wang WC, Kovnar EH, Tonkin IL, et al. High risk of recurrent stroke after discontinuance of five to twelve years of tranfusion therapy in patients with sickle cell disease. J Pediatr 1991; 118: 377-82.
13. Serjeant GR. Chronic tranfusion regimes in sickly cell disease: problem of panacea? Br J Haematol 1997; 97: 253-55.
14. Adams R, McKie V, Nichols F, et al. The use of transcranial ultrasonography to predict stroke in sickle cell disease. N Engl J Med 1992; 326: 605-10.
15. Robertson PL, Aldrich MS, Hanash SM, Goldstein GW. Stroke associated with obstructive sleep apnoea in a child with sickle cell anemia. Ann Neurol 1988; 23: 614-16.
16. Serjeant GR, De Ceulaer C, Lethbridge R, Morris JS, Singhal A, Thomas PW. The painful crisis of homozygous sickle cell disease - clinical features. Br J Haematol 1994; 87: 586-91.
17. Poncz M, Kane E, Gill FM. Acute chest syndrome in sickle cell disease: etiology and clinical correlates. J Pediatr 1985; 107: 861-66.
18. Sprinkle RH, Cole T, Smith S, Buchanan GR. Acute chest syndrome in children with sickle cell disease: a retrospective analysis of 100 hospitalized cases. Am J Pediatr Hematol/Oncol 1986; 8: 105-10.
19. Vichinsky E, Williams R, Das M, et al. Pulmonary fat embolism: a distinct cause of severe acute chest syndrome in sickle cell anemia. Blood 1994; 83: 3107-12.
20. Mallouh AA, Asha MI. Beneficial effect of blood transfusion in children with sickle cell chest syndrome. Am J Dis Child 1988: 142: 178-82.
21. Rucknagel DL, Kalinyak KA, Gelfand Mj. Rib infarcts and acute chest syndrome in sickle cell diseases. Lancet 1991; 337: 831-33.
22. Bekllket PS, Kalinyak KA, Shuckla R, Gelfand MJ, Rucknagel DL. Incentive spirometry to prevent acute pulmonary complications in sickle cell diseases. N Engl J Med 1995; 333: 699-703.
23. Serjeant GR, De Ceulaer K, Maude GH. Stilboestrol and stuttering priapism, in homozygous sickle cell disease. Lancet 1985; ii: 1274-76.
24. Vichinsky EP, Haberkern CM, Neumayr L, et al. A comparison of conservative and agressive tranfusion regimes in the perioperative management of sickle cell disease. N Engl J Med 1995; 333: 206-13.
25. Serjeant GR. Fetal haemoglobin in homozygous sickle cell disease. Clin Haematol 1975; 4: 109-22.
26. Higgs DR, Aldridge BE, Lamb J, et al. The interaction of alpha-thalassemia and homozygous sickle-cell disease. N Engl J Med 1982; 306: 1441-46.
27. Baum KF, Dunn DT, Maude GH, Serjeant GR. The painful crisis of homozygous sickle cell disease: a study of risk factors. Arch Intern Med 1987; 147: 1231-34.
28. Platt OS, Thorington BD, Brambilla DJ, et al. Pain in sickle cell disease: rates and risk factors. N Engl J Med 1991; 325: 11-16.
29. Serjeant G, Serjeant B, Stephens A, et al. Determinants of haemoglobin level in steady-state homozygous sickle cell disease. Br J Haematol 1996; 92: 143-49.
30. Charache S, Terrin ML, Moore RD, et al. Effect of hydroxyurea on the frequency of painful crises in sickle cell anemia. N Engl J Med 1995; 332: 1217-22.
31. Walters MC, Patience M, Leisenring W, et al. Bone marrow transplantation for sickle cell disease. N Engl J Med 1996; 335: 369-76.
32. Johnson FL, Look AT, Gockerman I, Ruggoero MR, Dalla-Pozza L, Billings FT. Bone-marrow transplantation in a patient with sickle-cell anemia. N Engl J Med 1984; 311: 780-83.
33. Lee A, Thomas P, Cupidore L, Serjeant B, Serjeant G. Improved survival in homozygous sickle cell disease: lessons from a cohort study. BMJ 1995; 311: 160-62.
34. Platt OS, Brambilla DJ, Ross WF. Mortality in sickle cell disease: life expectancy and risk factor for early death. N Engl J Med 1994; 330: 1639-44.