Gaucher disease: Assessment of skeletal involvement and therapeutic responses to enzyme replacement

Skeletal Radiology

Volumn 26, Issue 12, 1997, Pages 687-696

  Hermann, G ^a   Pastores, G M ^a,b,c   Abdelwahab, I F ^a   Lorberboym, A M ^a  

^a MOUNT SINAI MEDICAL CENTER   (United States)

^b MOUNT SINAI SCHOOL OF MEDICINE   (United States)

^c NEW YORK UNIVERSITY   (United States)

Author keywords

Gaucher disease type 1; Imaging CT; MRI, Gaucher disease; Skeletal changes, Gaucher disease

Indexed keywords

ALGLUCERASE; BISPHOSPHONIC ACID DERIVATIVE; IMIGLUCERASE; PAMIDRONIC ACID; RADIOISOTOPE; SULFUR;

BONE DISEASE; BONE MARROW DISEASE; BONE SCINTISCANNING; CLINICAL FEATURE; COMPUTER ASSISTED TOMOGRAPHY; DIAGNOSTIC APPROACH ROUTE; DIAGNOSTIC IMAGING; DISEASE ACTIVITY; ENZYME REPLACEMENT; GAUCHER DISEASE; GENE MUTATION; HUMAN; NUCLEAR MAGNETIC RESONANCE IMAGING; PATHOLOGY; PRIORITY JOURNAL; RADIOLOGY; REVIEW;

ADOLESCENT; ADULT; BONE AND BONES; BONE DISEASES; BONE MARROW; CHILD; FEMALE; GAUCHER DISEASE; GLUCOSYLCERAMIDASE; HUMANS; MAGNETIC RESONANCE IMAGING; MALE; RECOMBINANT PROTEINS; SPLENECTOMY; TOMOGRAPHY, X-RAY COMPUTED;

EID: 0031440938     PISSN: 03642348     EISSN: None     Source Type: Journal    
DOI: 10.1007/s002560050313     Document Type: Review

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