Genetics of prions

Annual Review of Genetics

Volumn 31, Issue , 1997, Pages 139-175

  Prusiner, Stanley B ^a   Scott, Michael R ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

Bovine spongiform encephalopathy; Human prion disease; PrP genes; Species barrier; Strains of prions

Indexed keywords

PRION PROTEIN;

BOVINE SPONGIFORM ENCEPHALOPATHY; CREUTZFELDT JAKOB DISEASE; DISEASE ASSOCIATION; DNA TEMPLATE; HUMAN; NONHUMAN; PATHOPHYSIOLOGY; PRIORITY JOURNAL; PROTEIN CONFORMATION; PROTEIN DETERMINATION; PROTEIN SYNTHESIS; REVIEW;

ANIMALS; FUNGAL PROTEINS; HUMANS; PRION DISEASES; PRIONS; VARIATION (GENETICS);

BOVINAE; MAMMALIA; OVIS ARIES;

EID: 0031437224     PISSN: 00664197     EISSN: None     Source Type: Book Series    
DOI: 10.1146/annurev.genet.31.1.139     Document Type: Review

References (15)

1. Aigle M, Lacroute F. 1975. Genetical aspects of [URE3], a non-Mendelian, cytoplasmically inherited mutation in yeast. Mol. Gen. Genet. 136:327-35
2. Alper T, Cramp WA, Haig DA, Clarke MC. 1967. Does the agent of scrapie replicate without nucleic acid? Nature 214:764-66
3. 2a. Anderson RM, Donnelly CA, Ferguson NM, Woolhouse MEJ, Watt CJ, et al. 1996. Transmission dynamics and epidemiology of BSE in British cattle. Nature 382:779-88
4. Baker HF, Ridley RM, Wells GAH. 1993. Experimental transmission of BSE and scrapie to the common marmoset. Vet. Rec. 132:403-6
5. Barry RA, Prusiner SB. 1986. Monoclonal antibodies to the cellular and scrapie prion proteins. J. Infect. Dis. 154:518-21
6. Basler K, Oesch B, Scott M, Westaway D, Wälchli M, et al. 1986. Scrapie and cellular PrP isoforms are encoded by the same chromosomal gene. Cell 46:417-28
7. Bertoni JM, Brown P, Goldfarb L, Gajdusek D, Omaha NE. 1992. Familial Creutzfeldt-Jakob disease with the PRNP codon 2001ys mutation and supranuclear palsy but without myoclonus or periodic EEG complexes. Neurology 42 (No. 4, Suppl. 3):350 (Abstr.)
8. Bessen RA, Kocisko DA, Raymond GJ, Nandan S, Lansbury PT, Caughey B. 1995. Non-genetic propagation of strain-specific properties of scrapie prion protein. Nature 375:698-700
9. Bessen RA, Marsh RF. 1994. Distinct PrP properties suggest the molecular basis of strain variation in transmissible mink encephalopathy. J. Virol. 68:7859-68
10. Bessen RA, Marsh RF. 1992. Identification of two biologically distinct strains of transmissible mink encephalopathy in hamsters. J. Gen. Virol. 73:329-34
11. Bessen RA, Marsh RF. 1992. Biochemical and physical properties of the prion protein from two strains of the transmissible mink encephalopathy agent. J. Virol. 66:2096-101
12. Billette de Villemeur T, Deslys J-P, Pradel A, Soubrié C, Alpérovitch A, et al. 1996. Creutzfeldt-Jakob disease from contaminated growth hormone extracts in France. Neurology 47:690-95
13. Bockman JM, Prusiner SB, Tateishi J, Kingsbury DT. 1987. Immunoblotting of Creutzfeldt-Jakob disease prion proteins: host species-specific epitopes. Ann. Neurol. 21:589-95
14. Bolton DC, McKinley MP, Prusiner SB. 1982. Identification of a protein that purifies with the scrapie prion. Science 218:1309-11
15. Bons N, Mestre-Francés N, Charnay Y, Tagliavini F. 1996. Spontaneous spongi-form encephalopathy in a young adult rhesus monkey. Lancet 348:55