Rapidly progressive autosomal dominant parkinsonism and dementia with pallido-ponto-nigral degeneration (PPND) and disinhibition-dementia- parkinsonism-amyotrophy complex (DDPAC) are clinically distinct conditions that are both linked to 17q21-22

Parkinsonism and Related Disorders

Volumn 3, Issue 2, 1997, Pages 67-76

  Wszolek, Zbigniew K ^a   Lynch, Timothy ^b   Wilhelmsen, Kirk C ^b,c,d  

^a UNIVERSITY OF NEBRASKA MEDICAL CENTER   (United States)

^b NEUROLOGICAL INSTITUTE   (United States)

^c UNIVERSITY OF CALIFORNIA   (United States)

^d SAN FRANCISCO GENERAL HOSPITAL   (United States)

Author keywords

Amyotrophy; Dementia; Disinhibition dementia parkinsonism amyotrophy complex (DDPAC); Linkage analysis 17q21 22; Parkinsonism; Rapidly progressive autosomal dominant parkinsonism and dementia with pallido ponto nigral degeneration (PPND)

Indexed keywords

ADULT; AGED; ARTICLE; AUTOSOMAL DOMINANT DISORDER; BRAIN DEGENERATION; CHROMOSOME 17Q; CONTROLLED STUDY; DEMENTIA; FAMILY; FEMALE; GENE LOCUS; GENE MUTATION; GENEALOGY; GENETIC ANALYSIS; GENETIC LINKAGE; GLOBUS PALLIDUS; HUMAN; MAJOR CLINICAL STUDY; MALE; MUSCLE ATROPHY; PARKINSONISM; PONS; PRIORITY JOURNAL; SUBSTANTIA NIGRA;

EID: 0031426061     PISSN: 13538020     EISSN: None     Source Type: Journal    
DOI: 10.1016/S1353-8020(97)00006-0     Document Type: Article

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