-
2
-
-
0025931429
-
-
Anderson, M., Berger, H., Rich, D., Gregory R., Smith, A., and Welsh, M. (1991a). Cell 67, 775-784.
-
(1991)
Cell
, vol.67
, pp. 775-784
-
-
Anderson, M.1
Berger, H.2
Rich, D.3
Gregory, R.4
Smith, A.5
Welsh, M.6
-
3
-
-
0025868103
-
-
Anderson, M., Gregory, R., Thompson, S., Souza, D., Paul, S., Mulligan, R., Smith, A., and Welsh, M. (1991b). Science 253, 202-205.
-
(1991)
Science
, vol.253
, pp. 202-205
-
-
Anderson, M.1
Gregory, R.2
Thompson, S.3
Souza, D.4
Paul, S.5
Mulligan, R.6
Smith, A.7
Welsh, M.8
-
4
-
-
0028174962
-
-
Baukrowitz, T., Hwang, T., Nairn, A., and Gadsby, D. (1994). Neuron 12, 473-482.
-
(1994)
Neuron
, vol.12
, pp. 473-482
-
-
Baukrowitz, T.1
Hwang, T.2
Nairn, A.3
Gadsby, D.4
-
6
-
-
0026532895
-
-
Bear, C., Li, C., Kartner, N., Bridges, R., Jensen, T., Ramjeesingh, M., and Riordan, J. (1992). Cell 68, 809-818.
-
(1992)
Cell
, vol.68
, pp. 809-818
-
-
Bear, C.1
Li, C.2
Kartner, N.3
Bridges, R.4
Jensen, T.5
Ramjeesingh, M.6
Riordan, J.7
-
7
-
-
0027519153
-
-
Berger, H. A., Travis, S. M., and Welsh, M. J. (1993). J. Biol. Chem. 268, 2037-2047.
-
(1993)
J. Biol. Chem.
, vol.268
, pp. 2037-2047
-
-
Berger, H.A.1
Travis, S.M.2
Welsh, M.J.3
-
8
-
-
0026026818
-
-
Bourne, H. R., Sanders, D. A., and McCormick, F. (1991). nature 349, 117-120.
-
(1991)
Nature
, vol.349
, pp. 117-120
-
-
Bourne, H.R.1
Sanders, D.A.2
McCormick, F.3
-
10
-
-
0027311276
-
-
Chang, X.-B., Tabcharani, J., Hou, Y.-X., Jensen, T., Kartner, N., Alon, N., Hanrahan, J., and Riordan, J. (1993). J. Biol. Chem. 268, 11304-11311.
-
(1993)
J. Biol. Chem.
, vol.268
, pp. 11304-11311
-
-
Chang, X.-B.1
Tabcharani, J.2
Hou, Y.-X.3
Jensen, T.4
Kartner, N.5
Alon, N.6
Hanrahan, J.7
Riordan, J.8
-
11
-
-
0025987020
-
-
Cheng, S., Rich, D., Marshall, J., Gregory, R., Welsh, M., and Smith, A. (1991). Cell 66, 1027-1036.
-
(1991)
Cell
, vol.66
, pp. 1027-1036
-
-
Cheng, S.1
Rich, D.2
Marshall, J.3
Gregory, R.4
Welsh, M.5
Smith, A.6
-
13
-
-
0028328645
-
-
Dulhanty, A. M., and Riordan, J. R., (1994). Biochemistry 33 (13), 4072-4079.
-
(1994)
Biochemistry
, vol.33
, Issue.13
, pp. 4072-4079
-
-
Dulhanty, A.M.1
Riordan, J.R.2
-
14
-
-
0018402806
-
-
Frizzell, R. A., Field, M., and Schultz, S. G. (1979). Am. J. Physiol. 236, F1-F8.
-
(1979)
Am. J. Physiol.
, vol.236
-
-
Frizzell, R.A.1
Field, M.2
Schultz, S.G.3
-
15
-
-
0027191065
-
-
Gabriel, S. E., Clarke, L. L., Boucher, R. C., and Stutts, M. J., (1993). Nature 363, 263-266.
-
(1993)
Nature
, vol.363
, pp. 263-266
-
-
Gabriel, S.E.1
Clarke, L.L.2
Boucher, R.C.3
Stutts, M.J.4
-
16
-
-
0027362241
-
-
Gout, I., Dhand, R., Hiles, I., Fry, M., Panayotou, G., Das, P., Truong, O., Totty, N., Hsuan, J., Booker, G., Campbell, I., and Waterfield, M. (1993). Cell 75, 25-36.
-
(1993)
Cell
, vol.75
, pp. 25-36
-
-
Gout, I.1
Dhand, R.2
Hiles, I.3
Fry, M.4
Panayotou, G.5
Das, P.6
Truong, O.7
Totty, N.8
Hsuan, J.9
Booker, G.10
Campbell, I.11
Waterfield, M.12
-
19
-
-
0026702994
-
-
Hartman, J., Huang, Z., Rado, T., Peng, S., Jilling, T., Muccio, D., and Sorscher, E. (1992). J. Biol. Chem. 267, 6455-6458.
-
(1992)
J. Biol. Chem.
, vol.267
, pp. 6455-6458
-
-
Hartman, J.1
Huang, Z.2
Rado, T.3
Peng, S.4
Jilling, T.5
Muccio, D.6
Sorscher, E.7
-
20
-
-
0027099661
-
-
Haws, C., Krouse, M. E., Xia, Y., Gruenert, D. C., and Wine, J. J. (1992). Am. J. Physiol. 263 (6 Pt. 1), L692-707.
-
(1992)
Am. J. Physiol.
, vol.263
, Issue.1-6 PART
-
-
Haws, C.1
Krouse, M.E.2
Xia, Y.3
Gruenert, D.C.4
Wine, J.J.5
-
21
-
-
0028340159
-
-
Hwang, T.-C., Nagel, G., Nairn, A., and Gadsby, D. (1994). Proc. Natl. Acad. Sci. USA 91, 4698-4702.
-
(1994)
Proc. Natl. Acad. Sci. USA
, vol.91
, pp. 4698-4702
-
-
Hwang, T.-C.1
Nagel, G.2
Nairn, A.3
Gadsby, D.4
-
22
-
-
0025374695
-
-
Hyde, S., Emsley, P., Hartshorn, M., Mimmack, M., Gileadi, U., Pearce, S., Gallanger, M., Gill, D., Hubbard, R., and Higgins, C. (1990). Nature 346, 362-365.
-
(1990)
Nature
, vol.346
, pp. 362-365
-
-
Hyde, S.1
Emsley, P.2
Hartshorn, M.3
Mimmack, M.4
Gileadi, U.5
Pearce, S.6
Gallanger, M.7
Gill, D.8
Hubbard, R.9
Higgins, C.10
-
23
-
-
0028972501
-
-
Inagaki, N., Gonoi, T., Clement, J., Namba, N., Inazawa, J., Gonzalez, G., Aguilar-Bryan, L., Seina, S., and Bryan, J. (1995). Science 270, 1166-1169.
-
(1995)
Science
, vol.270
, pp. 1166-1169
-
-
Inagaki, N.1
Gonoi, T.2
Clement, J.3
Namba, N.4
Inazawa, J.5
Gonzalez, G.6
Aguilar-Bryan, L.7
Seina, S.8
Bryan, J.9
-
24
-
-
0026073070
-
-
Kartner, N., Hanrahan, J., Jensen, T., Naismith, L., Sun, S., Ackerley, C., Reyes, E., L-C. Tsui, Rommens, J. M., Bear, C. E., and Riordan, J. R. (1991). Cell 64, 681-691.
-
(1991)
Cell
, vol.64
, pp. 681-691
-
-
Kartner, N.1
Hanrahan, J.2
Jensen, T.3
Naismith, L.4
Sun, S.5
Ackerley, C.6
Reyes, E.7
Tsui, L.-C.8
Rommens, J.M.9
Bear, C.E.10
Riordan, J.R.11
-
25
-
-
0025874599
-
-
Knowles, M. R., Clarke, L. L., and Boucher, R. C. (1991). N. Engl. J. Med. 325, 533-538.
-
(1991)
N. Engl. J. Med.
, vol.325
, pp. 533-538
-
-
Knowles, M.R.1
Clarke, L.L.2
Boucher, R.C.3
-
27
-
-
0028360128
-
-
Ko, Y. H., Thomas, P. J., and Pedersen, P. L. (1994). J. Biol. Chem. 269 (20), 14584-14588.
-
(1994)
J. Biol. Chem.
, vol.269
, Issue.20
, pp. 14584-14588
-
-
Ko, Y.H.1
Thomas, P.J.2
Pedersen, P.L.3
-
28
-
-
15844392129
-
-
Li, C., Ramjeesingh, M., and Bear, C. E. (1996a). J. Biol. Chem. 271, 11623-11626.
-
(1996)
J. Biol. Chem.
, vol.271
, pp. 11623-11626
-
-
Li, C.1
Ramjeesingh, M.2
Bear, C.E.3
-
29
-
-
0029904733
-
-
Li, C., Ramjeesingh, M., Wang, W., Garami, E., Hewryk, M., Lee, D., Rommens, J. M., Galley, K., and Bear, C. E. (1996b). J. Biol. Chem. 271, 28463-28468.
-
(1996)
J. Biol. Chem.
, vol.271
, pp. 28463-28468
-
-
Li, C.1
Ramjeesingh, M.2
Wang, W.3
Garami, E.4
Hewryk, M.5
Lee, D.6
Rommens, J.M.7
Galley, K.8
Bear, C.E.9
-
31
-
-
0029871744
-
-
Ma, J., Tasch, J. E., Tao, T., Zhao, J., Xie, J., Drumm, M. L., and Davis, P. B., (1996). J. Biol. Chem. 271(13) 7351-6.
-
(1996)
J. Biol. Chem.
, vol.271
, Issue.13
, pp. 7351-7356
-
-
Ma, J.1
Tasch, J.E.2
Tao, T.3
Zhao, J.4
Xie, J.5
Drumm, M.L.6
Davis, P.B.7
-
32
-
-
0029058027
-
-
Manavalan, P., Dearborn, D., McPherson, J., and Smith, A. (1995). FEBS Lett. 366, 87-91.
-
(1995)
FEBS Lett.
, vol.366
, pp. 87-91
-
-
Manavalan, P.1
Dearborn, D.2
McPherson, J.3
Smith, A.4
-
33
-
-
0026053770
-
-
Mimura, C., Holbrook, S., and Ames, G. (1991). Proc. Natl. Acad. Sci. USA 88, 84-88.
-
(1991)
Proc. Natl. Acad. Sci. USA
, vol.88
, pp. 84-88
-
-
Mimura, C.1
Holbrook, S.2
Ames, G.3
-
34
-
-
0028236014
-
-
Prince, L. S., Workman, R. B., Jr., and Marchase, R. B. (1994). Proc. Natl. Acad. Sci. USA 91, 5192-5196.
-
(1994)
Proc. Natl. Acad. Sci. USA
, vol.91
, pp. 5192-5196
-
-
Prince, L.S.1
Workman Jr., R.B.2
Marchase, R.B.3
-
36
-
-
0004039643
-
-
Academic Press, Orlando, Florida, Chapter 2
-
Racker, E. (1985). Reconstitution of Transporters, Receptors, and Pathological States, Academic Press, Orlando, Florida, Chapter 2, p. 37.
-
(1985)
Reconstitution of Transporters, Receptors, and Pathological States
, pp. 37
-
-
Racker, E.1
-
37
-
-
6844256056
-
-
Ramjeesingh, M., Li, C., Wang, W., and Bear, C. E. (1995). Ped. Pulmonol. S12, A33.
-
(1995)
Ped. Pulmonol.
, vol.S12
-
-
Ramjeesingh, M.1
Li, C.2
Wang, W.3
Bear, C.E.4
-
38
-
-
0027937589
-
-
Reisin, I. L., Prat, A. G., Abraham, E. H., Amara, J. F., Gregory, R. J., Ausiello, D. A., and Cantiello, H. F. (1994). J. Biol. Chem. 269, 20584-20591.
-
(1994)
J. Biol. Chem.
, vol.269
, pp. 20584-20591
-
-
Reisin, I.L.1
Prat, A.G.2
Abraham, E.H.3
Amara, J.F.4
Gregory, R.J.5
Ausiello, D.A.6
Cantiello, H.F.7
-
39
-
-
0024424270
-
-
Riordan, J., Rommens, J., Kerem, B.-S., Noa, A., Rozmahel, R., Grzelczak, Z., Zielenski, J., Lok, S., Plavsic, N., Jia-Ling Chou, Drumm, M., Iannuzzi, M., Collins, F., and Tsui, L.-C. (1989). Science 245, 1066-1073.
-
(1989)
Science
, vol.245
, pp. 1066-1073
-
-
Riordan, J.1
Rommens, J.2
Kerem, B.-S.3
Noa, A.4
Rozmahel, R.5
Grzelczak, Z.6
Zielenski, J.7
Lok, S.8
Plavsic, N.9
Chou, J.-L.10
Drumm, M.11
Iannuzzi, M.12
Collins, F.13
Tsui, L.-C.14
-
40
-
-
13344282728
-
-
Rozmahel, R., Wilschanski, M., Plyte, S., Oliver, N., Auerbach, W., Moore, A., Wuerst, W., Joyner, A., Firstner, J., Durie, P., Bear, C., and Tsui, L-C. (1996). Nature Genet. 12(3), 280-287.
-
(1996)
Nature Genet.
, vol.12
, Issue.3
, pp. 280-287
-
-
Rozmahel, R.1
Wilschanski, M.2
Plyte, S.3
Oliver, N.4
Auerbach, W.5
Moore, A.6
Wuerst, W.7
Joyner, A.8
Firstner, J.9
Durie, P.10
Bear, C.11
Tsui, L.-C.12
-
41
-
-
0028980536
-
-
Schweibert, E. M., Egan, M. E., Hwang, T-H., Fulmer, S. B., Allen, S. S., Cutting, G. R., and Guggino, W. B. (1995). Cell 81, 1063-1073.
-
(1995)
Cell
, vol.81
, pp. 1063-1073
-
-
Schweibert, E.M.1
Egan, M.E.2
Hwang, T.-H.3
Fulmer, S.B.4
Allen, S.S.5
Cutting, G.R.6
Guggino, W.B.7
-
42
-
-
0028940488
-
-
Senior A. E., al-Shawi, M. K., and Urbatsch, I. L. (1995a). J. Bioenerg. Biomembr. 27, 31-36, ??
-
(1995)
J. Bioenerg. Biomembr.
, vol.27
, pp. 31-36
-
-
Senior, A.E.1
Al-Shawi, M.K.2
Urbatsch, I.L.3
-
43
-
-
0029559159
-
-
Senior, A. E., al-Shawi, M. K., and Urbatsch, I. L. (1995b). FEBS Lett. 377 (3), 285-289.
-
(1995)
FEBS Lett.
, vol.377
, Issue.3
, pp. 285-289
-
-
Senior, A.E.1
Al-Shawi, M.K.2
Urbatsch, I.L.3
-
46
-
-
0029027674
-
-
Sharom, F., Xiaohong, Y., J, C., and CA, Doige. (1995a). Biochem. J. 308, 381-390.
-
(1995)
Biochem. J.
, vol.308
, pp. 381-390
-
-
Sharom, F.1
Xiaohong, Y.2
J, C.3
Doige, C.A.4
-
47
-
-
0028920219
-
-
Sharom, F. J. Sharom, DiDiodato, G., Yu, Xiaohong, and Ash- bourne, K. J. D. (1995b). J. Biol. Chem. 270, 10334-10341.
-
(1995)
J. Biol. Chem.
, vol.270
, pp. 10334-10341
-
-
Sharom, F.1
Sharom, J.2
DiDiodato, G.3
Yu, X.4
Ash-bourne, K.J.D.5
-
48
-
-
0026649122
-
-
Snouwaert, J. N., Brigman, K. K., Latour, A. M., Malouf, N. N., Boucher, R. C., Smithies, O., and Koller, B. H. (1992). Science 257, 1083-1088.
-
(1992)
Science
, vol.257
, pp. 1083-1088
-
-
Snouwaert, J.N.1
Brigman, K.K.2
Latour, A.M.3
Malouf, N.N.4
Boucher, R.C.5
Smithies, O.6
Koller, B.H.7
-
49
-
-
0028029015
-
-
Stutts, M. J., Fitz, J. G., Paradiso, A. M., and Boucher, R. C. (1994). Am. J. Physiol. 267, C1442-C1451.
-
(1994)
Am. J. Physiol.
, vol.267
-
-
Stutts, M.J.1
Fitz, J.G.2
Paradiso, A.M.3
Boucher, R.C.4
-
50
-
-
0028982894
-
-
Stutts, M. J., Canessa, C. M., Olsen, J. C., Hamrick, M., Cohn, J. A., Rossier, B. C., and Boucher, R. C. (1995). Science 269, 847-850.
-
(1995)
Science
, vol.269
, pp. 847-850
-
-
Stutts, M.J.1
Canessa, C.M.2
Olsen, J.C.3
Hamrick, M.4
Cohn, J.A.5
Rossier, B.C.6
Boucher, R.C.7
-
51
-
-
0025002910
-
-
Tabcharani, J., Lowe, W., Elie, D., and Hanrahan, J. (1990). FEBS Lett 270, 157-164.
-
(1990)
FEBS Lett
, vol.270
, pp. 157-164
-
-
Tabcharani, J.1
Lowe, W.2
Elie, D.3
Hanrahan, J.4
-
52
-
-
0025885376
-
-
Tabcharani, J. A., Chang, X.-B., Riordan, J. R., and Hanrahan, J. W. (1991). Nature 352, 628-631.
-
(1991)
Nature
, vol.352
, pp. 628-631
-
-
Tabcharani, J.A.1
Chang, X.-B.2
Riordan, J.R.3
Hanrahan, J.W.4
-
53
-
-
0026629383
-
-
Tabcharani, J. A., Chang, X.-B., Riordan, J. R., and Hanrahan, J. W. (1992). Biophys. J. 62, 1-4.
-
(1992)
Biophys. J.
, vol.62
, pp. 1-4
-
-
Tabcharani, J.A.1
Chang, X.-B.2
Riordan, J.R.3
Hanrahan, J.W.4
-
54
-
-
0027423190
-
-
Tabcharani, J., Rommens, J., Hou, Y., Chang, X.-B., Tsui, L., Riordan, J., and Hanrahan, J. (1993). Nature 366, 79-82.
-
(1993)
Nature
, vol.366
, pp. 79-82
-
-
Tabcharani, J.1
Rommens, J.2
Hou, Y.3
Chang, X.-B.4
Tsui, L.5
Riordan, J.6
Hanrahan, J.7
-
55
-
-
0025906334
-
-
Thomas, P., Shenbagamurthi, T., Ysern, X., and Pedersen, P. (1991). Science 251, 555-557.
-
(1991)
Science
, vol.251
, pp. 555-557
-
-
Thomas, P.1
Shenbagamurthi, T.2
Ysern, X.3
Pedersen, P.4
-
56
-
-
0027179469
-
-
Travis, S., Carson, M., Ries, D., and Welsh, M. (1993). J. Biol. Chem. 268, 15336-15339.
-
(1993)
J. Biol. Chem.
, vol.268
, pp. 15336-15339
-
-
Travis, S.1
Carson, M.2
Ries, D.3
Welsh, M.4
-
59
-
-
0003720078
-
-
(Scriver, C. R., Beaudet, A. L., Sly, W. S., and Valle, D., eds.), McGraw-Hill, New York
-
Welsh, M., Tsui, L.-C., Boat, T. F., and Beaudet, A. L. (1995). Cystic Fibrosis in the Metabolic and Molecular Bases of Inherited Disease, 7th edn. (Scriver, C. R., Beaudet, A. L., Sly, W. S., and Valle, D., eds.), McGraw-Hill, New York, pp. 3799-3876.
-
(1995)
Cystic Fibrosis in the Metabolic and Molecular Bases of Inherited Disease, 7th Edn.
, pp. 3799-3876
-
-
Welsh, M.1
Tsui, L.-C.2
Boat, T.F.3
Beaudet, A.L.4
-
60
-
-
0028265949
-
-
Winter, M., Sheppard, D., Carson, M., and Welsh, M. (1994). Biophys. J. 66, 1398-1403.
-
(1994)
Biophys. J.
, vol.66
, pp. 1398-1403
-
-
Winter, M.1
Sheppard, D.2
Carson, M.3
Welsh, M.4
|