Hb S/Hb Lepore with mild sickling symptoms: A hemoglobin variant with mostly δ-chain sequences ameliorates sickle-cell disease

American Journal of Hematology

Volumn 54, Issue 2, 1997, Pages 164-165

  Fairbanks, V F ^a   McCormick, D J ^a   Kubik, K S ^a   Rezuke, W N ^b   Black, D ^c   Ochaney, M S ^d   Schwartz, D ^d  

^a MAYO CLINIC   (United States)

^b HARTFORD HOSPITAL   (United States)

^c UNIVERSITY OF CONNECTICUT   (United States)

^d North Arundel Hospital   (United States)

Author keywords

delta chain; Hb A2; Hb Lepore; Hb S; sickle cell disease

Indexed keywords

HEMOGLOBIN;

ADOLESCENT; ADULT; ARTICLE; CASE REPORT; CELL MEMBRANE; ERYTHROCYTE; FEMALE; HEMOLYSIS; HUMAN; MALE; MICROCYTOSIS; PRIORITY JOURNAL; SICKLE CELL ANEMIA;

ADOLESCENT; ADULT; ANEMIA, SICKLE CELL; FEMALE; HEMOGLOBIN, SICKLE; HEMOGLOBINS; HEMOGLOBINS, ABNORMAL; HUMANS; MALE; VARIATION (GENETICS);

EID: 0031049681     PISSN: 03618609     EISSN: None     Source Type: Journal    
DOI: 10.1002/(SICI)1096-8652(199702)54:2<164::AID-AJH12>3.0.CO;2-F     Document Type: Article

References (5)

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5. Silvestroni E, Bianco I, Baglioni C: Interaction of hemoglobin Lepore with sickle cell trait and microcythemia (thalassemia) in a Southern Italian family. Blood 25:457-469, 1965.