Expression, purification and kinetic characterization of wild-type human ornithine transcarbamylase and a recurrent mutant that produces 'late onset' hyperammonaemia

Biochemical Journal

Volumn 322, Issue 2, 1997, Pages 625-631

  Morizono, Hiroki ^a   Tuchman, Mendel ^b   Rajagopal, Basavapatna S ^b   McCann, Mark T ^b   Listrom, Chad D ^a   Yuan, Xiaoling ^a,d   Venugopal, Divakaramenon ^c,e   Barany, George ^c   Allewell, Norma M ^a  

^a UNIVERSITY OF MINNESOTA   (United States)

^b UNIVERSITY OF MINNESOTA MEDICAL SCHOOL   (United States)

^c University of Minnesota   (United States)

^d New York Blood Center ^*  (United States)

^e NEW YORK BLOOD CENTER   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ASPARTATE CARBAMOYLTRANSFERASE; ORNITHINE; ORNITHINE CARBAMOYLTRANSFERASE;

ARTICLE; CRYSTAL STRUCTURE; ENZYME ACTIVE SITE; ENZYME DEFICIENCY; ENZYME KINETICS; ENZYME PURIFICATION; ESCHERICHIA COLI; GEL CHROMATOGRAPHY; GENE MUTATION; HUMAN; HYPERAMMONEMIA; MOLECULAR CLONING; PHYSIOLOGY; PRIORITY JOURNAL; PSEUDOMONAS AERUGINOSA; SEQUENCE HOMOLOGY; THERMOSTABILITY;

EID: 0031043291     PISSN: 02646021     EISSN: None     Source Type: Journal    
DOI: 10.1042/bj3220625     Document Type: Article

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