The mannosidoses and ceroid-lipofuscinoses: Experimental studies on two types of storage disease

Pathology

Volumn 29, Issue 1, 1997, Pages 51-56

  Jolly, Robert D ^a  

^a MASSEY UNIVERSITY   (New Zealand)

Author keywords

Batten disease; Ceroid lipofuscinosis; Glycoprotein; Lysosomes; Mannosidosis; Mitochondrial ATP synthase; Storage disease; Subunit c

Indexed keywords

ALPHA MANNOSIDASE; BETA MANNOSIDASE; GLYCOPROTEIN; INDOLIZIDINE ALKALOID; PROTEIN SUBUNIT; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATE SYNTHASE; SWAINSONINE;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; AUSTRALIA; BONE MARROW TRANSPLANTATION; CATABOLISM; CATTLE; COMPARATIVE STUDY; GLYCOSYLATION; HYDROPHOBICITY; INTOXICATION; LIPID PEROXIDATION; LIPOFUSCINOSIS; LYSOSOME STORAGE DISEASE; MANNOSIDOSIS; MITOCHONDRION; NEURONAL CEROID LIPOFUSCINOSIS; NONHUMAN; PROTEIN DEGRADATION; SHEEP;

EID: 0030981345     PISSN: 00313025     EISSN: None     Source Type: Journal    
DOI: 10.1080/00313029700169534     Document Type: Article

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