Succinyl-CoA:3-ketoacid coenzyme A transferase (SCOT): Development of an antibody to human SCOT and diagnostic use in hereditary SCOT deficiency

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1360, Issue 2, 1997, Pages 151-156

  Song, Xiang Qian ^a   Fukao, Toshiyuki ^a   Mitchell, Grant A ^b   Kassovska Bratinova, Sacha ^b,c   Ugarte, Magdalena ^d   Wanders, Ronald J A ^e   Hirayama, Ken ^f   Shintaku, Haruo ^g   Churchill, Perry ^h   Watanabe, Hiroh ^a   Orii, Tadao ⁱ   Kondo, Naomi ^a  

^a GIFU UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^b UNIVERSITY OF MONTREAL   (Canada)

^c HOSPITAL FOR SICK CHILDREN   (Canada)

^d UNIVERSIDAD AUTÓNOMA DE MADRID   (Spain)

^e Universiry Hospital Amsterdam   (Netherlands)

^f Izumi Municipal Hospital   (Japan)

^g OSAKA CITY UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

^h UNIVERSITY OF ALABAMA   (United States)

ⁱ Chubu Women's College   (Japan)

Author keywords

Antibody; Coenzyme A transferase; Immunoblot analysis; Inborn error of metabolism; Ketone body

Indexed keywords

3 OXOACID COENZYME A TRANSFERASE; ANTIBODY; KETONE BODY;

ANTIBODY PRODUCTION; ARTICLE; CONTROLLED STUDY; ENZYME DEFICIENCY; FIBROBLAST; GENE CONSTRUCT; GENE EXPRESSION; HUMAN; HUMAN CELL; IMMUNOBLOTTING; INBORN ERROR OF METABOLISM; LYMPHOCYTE; MOLECULAR CLONING; NONHUMAN; PRIORITY JOURNAL; RABBIT;

ANIMALS; BLOTTING, WESTERN; COENZYME A-TRANSFERASES; HUMANS; IMMUNOASSAY; KETONE BODIES; LIPID METABOLISM, INBORN ERRORS; RATS; RECOMBINANT PROTEINS;

BACTERIA (MICROORGANISMS); ORYCTOLAGUS CUNICULUS;

EID: 0030980629     PISSN: 09254439     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0925-4439(96)00074-9     Document Type: Article

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