Glycosaminoglycan storage in cultured neonatal murine mucopolysaccharidosis type VII neuroglial cells and correction by β- glucuronidase gene transfer

Journal of Neurochemistry

Volumn 68, Issue 5, 1997, Pages 2079-2085

  Taylor, Rosanne M ^a,b   Wolfe, John H ^a  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

^b UNIVERSITY OF SYDNEY   (Australia)

Author keywords

Glycosaminoglycans; Lysosomal storage disease; Mucopolysaccharidosis; Primary brain cell culture; Retrovirus vector; Glucuronidase

Indexed keywords

BETA GLUCURONIDASE; COMPLEMENTARY DNA; GLYCOSAMINOGLYCAN; VIRUS VECTOR;

ANIMAL CELL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; ENZYME ACTIVITY; ENZYME DEFICIENCY; ENZYME SUBSTRATE; GENE TRANSFER; GLIA; LYSOSOME; MOUSE; MUCOPOLYSACCHARIDOSIS TYPE 7; NEWBORN; NONHUMAN; PRIORITY JOURNAL; RETROVIRUS;

ANIMALIA; GILA; MURINAE; UNIDENTIFIED RETROVIRUS;

EID: 0030959573     PISSN: 00223042     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.1471-4159.1997.68052079.x     Document Type: Article

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