Accumulation of mitochondrial ATP synthase subunit c in muscle in a patient with neuronal ceroid lipofuscinosis (late infantile form)

Acta Neuropathologica

Volumn 93, Issue 6, 1997, Pages 628-632

  Umehara, Fujio ^a   Higuchi, Itsuro ^a   Tanaka, Kenji ^a   Niiyama, Takahito ^a   Ezaki, Junji ^b   Kominami, Eiki ^b   Osame, Mitsuhiro ^a  

^a KAGOSHIMA UNIVERSITY   (Japan)

^b JUNTENDO UNIVERSITY SCHOOL OF MEDICINE   (Japan)

Author keywords

Curvilinear profile; Mitochondrial ATP synthase subunit c; Muscle; Neuronal ceroid lipofuscinosis; Sural nerve

Indexed keywords

ACID PHOSPHATASE; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATE SYNTHASE;

ADULT; ARTICLE; BIOACCUMULATION; CASE REPORT; DIAGNOSTIC VALUE; ELECTRON MICROSCOPY; ENDOTHELIUM CELL; ENZYME SUBUNIT; FEMALE; FIBROBLAST; HUMAN; HUMAN TISSUE; IMMUNOHISTOCHEMISTRY; MUSCLE; NEURONAL CEROID LIPOFUSCINOSIS; PERINEURIUM; PRIORITY JOURNAL; SCHWANN CELL; SKELETAL MUSCLE; SMOOTH MUSCLE FIBER; SURAL NERVE;

ADULT; CYTOPLASMIC GRANULES; FEMALE; HUMANS; IMMUNOHISTOCHEMISTRY; MITOCHONDRIA, MUSCLE; MUSCLE, SKELETAL; NEURONAL CEROID-LIPOFUSCINOSES; PROTON-TRANSLOCATING ATPASES; SURAL NERVE;

EID: 0030923672     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s004010050661     Document Type: Article

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