A five-generation family with late-onset progressive hereditary hearing impairment due to cochleosaccular degeneration

Audiology and Neuro-Otology

Volumn 2, Issue 3, 1997, Pages 139-154

  Lalwani, Anil K ^a   Linthicum, Fred H ^b   Wilcox, Edward R ^c   Moore, Jean K ^b   Walters, Frederick C ^a   Agustin, Theresa B San ^c   Misiinski, J ^b   Miller, M R ^b   Sinninger, Yvonne ^b   Attaie, Ali ^a   Luxford, William M ^b  

^a UNIVERSITY OF CALIFORNIA   (United States)

^b HOUSE EAR INSTITUTE   (United States)

^c NATIONAL INSTITUTE ON DEAFNESS AND OTHER COMMUNICATION DISORDERS   (United States)

Author keywords

Linkage analysis; Lod score; Scheibe degeneration; Temporal bone histopathology

Indexed keywords

ADULT; ARTICLE; BLOOD SAMPLING; BRAIN STEM; CASE REPORT; COCHLEA; COCHLEOSACCULAR DYSPLASIA; CONGENITAL DEAFNESS; FAMILY; GENETIC LINKAGE; HEARING LOSS; HEREDITY; HUMAN; MALE; ONSET AGE; PRIORITY JOURNAL; SACCULUS; SCHEIBE DEGENERATION; TEMPORAL BONE; TISSUE DEGENERATION;

EID: 0030908919     PISSN: 14203030     EISSN: None     Source Type: Journal    
DOI: 10.1159/000259237     Document Type: Article

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