Undersulfation of cartilage proteoglycans ex vivo and increased contribution of amino acid sulfur to sulfation in vitro in McAlister dysplasia/atelosteogenesis type 2

European Journal of Biochemistry

Volumn 248, Issue 3, 1997, Pages 741-747

  Rossi, Antonio ^a   Bonaventure, Jacky ^b   Delezoide, Anne Lise ^b   Superti Furga, Andrea ^c   Cetta, Giuseppe ^a  

^a UNIVERSITY OF PAVIA   (Italy)

^b HÔPITAL NECKER ENFANTS MALADES   (France)

^c UNIVERSITY OF ZURICH   (Switzerland)

Author keywords

Chondrocyte; Chondrodysplasia; Cysteine metabolism; Proteoglycan; Sulfate transporter

Indexed keywords

CARRIER PROTEIN; PROTEOGLYCAN;

ARTICLE; CARTILAGE CELL; CHONDRODYSPLASIA; CONTROLLED STUDY; EPIPHYSEAL CARTILAGE; FETUS; FIBROBLAST; HIGH PERFORMANCE LIQUID CHROMATOGRAPHY; HUMAN; HUMAN CELL; HUMAN TISSUE; IN VITRO STUDY; MUTATION; PRIORITY JOURNAL; PROTEOGLYCAN SYNTHESIS; SULFATION;

EID: 0030851128     PISSN: 00142956     EISSN: None     Source Type: Journal    
DOI: 10.1111/j.1432-1033.1997.t01-1-00741.x     Document Type: Article

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