Different hematological phenotypes caused by the interaction of triplicated α-globin genes and heterozygous 13-thalassemia

American Journal of Hematology

Volumn 55, Issue 2, 1997, Pages 83-88

  Camaschella, C ^a   Kattamis, A C ^b   Petroni, D ^a   Roetto, A ^a   Sivera, P ^a   Sbaiz, L ^a   Cohen, A ^b   Ohene Frempong, K ^b   Trifillis, P ^c   Surrey, S ^b   Fortina, P ^b,d  

^a UNIVERSITY OF TURIN   (Italy)

^b UNIVERSITY OF PENNSYLVANIA   (United States)

^c CYPRUS INSTITUTE OF NEUROLOGY AND GENETICS   (Cyprus)

^d CHILDREN S HOSPITAL OF PHILADELPHIA   (United States)

Author keywords

thalassemia; A globin gene; Modifier genes

Indexed keywords

ALPHA GLOBIN; BETA GLOBIN; HEMOGLOBIN A2; HEMOGLOBIN F;

ADULT; AGED; ARTICLE; BETA THALASSEMIA; BLOOD TRANSFUSION; CHILD; CLINICAL ARTICLE; FAMILY; FEMALE; GENE CLUSTER; GENE EXPRESSION; GENE LOCUS; GENE MUTATION; GENOTYPE; GLOBIN GENE; HETEROZYGOSITY; HUMAN; IRON DEFICIENCY ANEMIA; MALE; MICROCYTOSIS; PHENOTYPE; PRIORITY JOURNAL; SIBLING; SPLENECTOMY; SPLENOMEGALY;

ADULT; BETA-THALASSEMIA; FEMALE; GENE EXPRESSION REGULATION; GLOBINS; HEMOGLOBINOPATHIES; HETEROZYGOTE; HUMANS; MALE; MULTIGENE FAMILY; PEDIGREE; PHENOTYPE;

EID: 0030850053     PISSN: 03618609     EISSN: None     Source Type: Journal    
DOI: 10.1002/(SICI)1096-8652(199706)55:2<83::AID-AJH6>3.0.CO;2-Z     Document Type: Article

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