-
1
-
-
0025060810
-
Oxidative denaturation of red blood cells in thalassemia
-
Shinar, E., and E.A. Rachmilewitz. 1990. Oxidative denaturation of red blood cells in thalassemia. Semin. Hematol. 27:70-82.
-
(1990)
Semin. Hematol.
, vol.27
, pp. 70-82
-
-
Shinar, E.1
Rachmilewitz, E.A.2
-
2
-
-
0027232102
-
Effect of excess α-hemoglobin chains on cellular and membrane oxidation in model β-thalassemic erythrocytes
-
Scott, M.D., J.J.M. van den Berg, T. Repka, P. Rouyer-Fessard, R.P. Hebbel, Y. Beuzard, and B.H. Lubin. 1993. Effect of excess α-hemoglobin chains on cellular and membrane oxidation in model β-thalassemic erythrocytes. J. Clin. Invest. 91:1706-1712.
-
(1993)
J. Clin. Invest.
, vol.91
, pp. 1706-1712
-
-
Scott, M.D.1
Van Den Berg, J.J.M.2
Repka, T.3
Rouyer-Fessard, P.4
Hebbel, R.P.5
Beuzard, Y.6
Lubin, B.H.7
-
3
-
-
0027429655
-
Nonrandom association of free iron with membranes of sickle and β-thalassemic erythrocytes
-
Repka, T., O. Shalev, R. Reddy, J. Yuan, A. Abrahamov, E.A. Rachmilewitz, P.S. Low, and R.P. Hebbel. 1993. Nonrandom association of free iron with membranes of sickle and β-thalassemic erythrocytes. Blood. 82:3204-3210.
-
(1993)
Blood
, vol.82
, pp. 3204-3210
-
-
Repka, T.1
Shalev, O.2
Reddy, R.3
Yuan, J.4
Abrahamov, A.5
Rachmilewitz, E.A.6
Low, P.S.7
Hebbel, R.P.8
-
4
-
-
0026597441
-
Oxidative red blood cell membrane injury in the pathophysiology of severe mouse β-thalassemia
-
Advani, R., E. Rubin, N. Mohandas, and S.L. Schrier. 1992. Oxidative red blood cell membrane injury in the pathophysiology of severe mouse β-thalassemia. Blood. 79:1064-1067.
-
(1992)
Blood
, vol.79
, pp. 1064-1067
-
-
Advani, R.1
Rubin, E.2
Mohandas, N.3
Schrier, S.L.4
-
5
-
-
0028282433
-
Oxidative damage and erythrocyte membrane transport abnormalities in thalassemias
-
Olivieri, O., L. De Franceschi, M.D. Capellini, D. Girelli, R. Corrocher, and C. Brugnara. 1994. Oxidative damage and erythrocyte membrane transport abnormalities in thalassemias. Blood. 84:315-320.
-
(1994)
Blood
, vol.84
, pp. 315-320
-
-
Olivieri, O.1
De Franceschi, L.2
Capellini, M.D.3
Girelli, D.4
Corrocher, R.5
Brugnara, C.6
-
6
-
-
0023781675
-
Nonheme iron in sickle erythrocyte membranes: Association with phospholipids and potential role in lipid peroxidation
-
Kuross, S.A., and R.P. Hebbel. 1988. Nonheme iron in sickle erythrocyte membranes: Association with phospholipids and potential role in lipid peroxidation. Blood. 72:1278-1285.
-
(1988)
Blood
, vol.72
, pp. 1278-1285
-
-
Kuross, S.A.1
Hebbel, R.P.2
-
7
-
-
0025749683
-
Hydroxyl radical formation by sickle erythrocyte membranes: Role of pathologic iron deposits and cytoplasmic reducing agents
-
Repka, T., and R.P. Hebbel. 1991. Hydroxyl radical formation by sickle erythrocyte membranes: role of pathologic iron deposits and cytoplasmic reducing agents. Blood. 78:2753-2758.
-
(1991)
Blood
, vol.78
, pp. 2753-2758
-
-
Repka, T.1
Hebbel, R.P.2
-
8
-
-
0025061081
-
The sickle erythrocyte in double jeopardy: Autoxidation and iron decompartmentalization
-
Hebbel, R.P. 1990. The sickle erythrocyte in double jeopardy: autoxidation and iron decompartmentalization. Semin. Hematol. 27:51-69.
-
(1990)
Semin. Hematol.
, vol.27
, pp. 51-69
-
-
Hebbel, R.P.1
-
9
-
-
0028898064
-
Iron-chelation therapy with oral deferiprone in patients with thalassemia major
-
Olivieri, N.F., G.M. Brittenham, D. Matsui, M. Berkovitch, L.M. Blendis, R.G. Cameron, R.A. McClelland, P.P. Liu, D.M. Templeton, and G. Koren. 1995. Iron-chelation therapy with oral deferiprone in patients with thalassemia major. N. Engl. J. Med. 332:918-922.
-
(1995)
N. Engl. J. Med.
, vol.332
, pp. 918-922
-
-
Olivieri, N.F.1
Brittenham, G.M.2
Matsui, D.3
Berkovitch, M.4
Blendis, L.M.5
Cameron, R.G.6
McClelland, R.A.7
Liu, P.P.8
Templeton, D.M.9
Koren, G.10
-
10
-
-
0000234906
-
Structure/red blood cell permeability, activity of iron(III) chelator complexes
-
Kontoghiorghes, G.J. 1988. Structure/red blood cell permeability, activity of iron(III) chelator complexes. Inorganic Chimica Acta. 151:101-106.
-
(1988)
Inorganic Chimica Acta
, vol.151
, pp. 101-106
-
-
Kontoghiorghes, G.J.1
-
11
-
-
0029097965
-
Deferiprone (L1) chelates pathologic iron deposits from membranes of intact thalassemic and sickle red blood cells both in vitro and in vivo
-
Shalev, O., T. Repka, A. Goldfarb, L. Grinberg, A. Abrahamov, N.F. Olivieri, E.A. Rachmilewitz, and R.P. Hebbel. 1995. Deferiprone (L1) chelates pathologic iron deposits from membranes of intact thalassemic and sickle red blood cells both in vitro and in vivo. Blood. 86:2008-2013.
-
(1995)
Blood
, vol.86
, pp. 2008-2013
-
-
Shalev, O.1
Repka, T.2
Goldfarb, A.3
Grinberg, L.4
Abrahamov, A.5
Olivieri, N.F.6
Rachmilewitz, E.A.7
Hebbel, R.P.8
-
13
-
-
0020564074
-
A mouse model for beta-thalassemia
-
Skow, L.C., B.A. Burkhart, F.M. Johnson, R.A. Popp, D.M. Popp, S.Z. Goldberg, W.F. Anderson, L.B. Barnett, and S.E. Lewis. 1983. A mouse model for beta-thalassemia. Cell. 34:1043-1052.
-
(1983)
Cell
, vol.34
, pp. 1043-1052
-
-
Skow, L.C.1
Burkhart, B.A.2
Johnson, F.M.3
Popp, R.A.4
Popp, D.M.5
Goldberg, S.Z.6
Anderson, W.F.7
Barnett, L.B.8
Lewis, S.E.9
-
14
-
-
0028925757
-
Cation transport in mouse erythrocytes: Role of K+/Cl- cotransport in regulatory volume decrease
-
Armsby, C.C., C. Brugnara, and S.L. Alper. 1995. Cation transport in mouse erythrocytes: Role of K+/Cl-cotransport in regulatory volume decrease. Am. J. Physiol (Cell Physiol. 37) 268:C894-C902.
-
(1995)
Am. J. Physiol (Cell Physiol. 37)
, vol.268
-
-
Armsby, C.C.1
Brugnara, C.2
Alper, S.L.3
-
15
-
-
0023937376
-
Excess heme in sickle erythrocyte inside-out membranes: Possible role in thiol oxidation
-
Kuross, S., B.H. Rank, and R.P. Hebbel. 1988. Excess heme in sickle erythrocyte inside-out membranes: Possible role in thiol oxidation. Blood. 71: 876-882.
-
(1988)
Blood
, vol.71
, pp. 876-882
-
-
Kuross, S.1
Rank, B.H.2
Hebbel, R.P.3
-
16
-
-
0021799078
-
Abnormal redox status of membrane-protein thiols in sickle erythrocytes
-
Rank, B., J. Carlsson, and R.P. Hebbel. 1985. Abnormal redox status of membrane-protein thiols in sickle erythrocytes. J. Clin. Invest. 75:1531-1537.
-
(1985)
J. Clin. Invest.
, vol.75
, pp. 1531-1537
-
-
Rank, B.1
Carlsson, J.2
Hebbel, R.P.3
-
17
-
-
0027244739
-
Biotin labeling as an alternative nonradioactive approach to determination of red cell survival
-
Hoffman-Fezer, G., J. Mysliwietz, W. Mörtbauer, H.J. Zeitler, E. Eberle, U. Hönle, and S. Thierfelder. 1993. Biotin labeling as an alternative nonradioactive approach to determination of red cell survival. Ann. Hematol. 67:81-87.
-
(1993)
Ann. Hematol.
, vol.67
, pp. 81-87
-
-
Hoffman-Fezer, G.1
Mysliwietz, J.2
Mörtbauer, W.3
Zeitler, H.J.4
Eberle, E.5
Hönle, U.6
Thierfelder, S.7
-
18
-
-
0020530019
-
Osmotic gradient ektacytometry: Comprehensive characterization of red cell volume and surface maintenance
-
Clark, M.R., N. Mohandas, and S. Shohet. 1983. Osmotic gradient ektacytometry: comprehensive characterization of red cell volume and surface maintenance. Blood. 61:899-910.
-
(1983)
Blood
, vol.61
, pp. 899-910
-
-
Clark, M.R.1
Mohandas, N.2
Shohet, S.3
-
19
-
-
0024560085
-
Differing erythrocyte membrane skeletal protein defects in alpha and beta thalassemia
-
Shinar, E., E.A. Rachmilewitz, and S.E. Lux. 1989. Differing erythrocyte membrane skeletal protein defects in alpha and beta thalassemia. J. Clin. Invest. 83:404-410.
-
(1989)
J. Clin. Invest.
, vol.83
, pp. 404-410
-
-
Shinar, E.1
Rachmilewitz, E.A.2
Lux, S.E.3
-
20
-
-
0024823331
-
A study of membrane protein defects and α hemoglobin chains of red blood cells in human β thalassemia
-
Rouyer-Fessard, P., M.-C. Garel, C. Domenget, D. Guetarni, D. Bachir, P. Colonna, and Y. Beuzard. 1989. A study of membrane protein defects and α hemoglobin chains of red blood cells in human β thalassemia. J. Biol. Chem. 264:19092-19098.
-
(1989)
J. Biol. Chem.
, vol.264
, pp. 19092-19098
-
-
Rouyer-Fessard, P.1
Garel, M.-C.2
Domenget, C.3
Guetarni, D.4
Bachir, D.5
Colonna, P.6
Beuzard, Y.7
-
21
-
-
0025224874
-
Mouse β thalassemia, a model for the membrane defects of erythrocytes in the human disease
-
Rouyer-Fessard, P., K. Leroy-Viard, C. Domenget, A. Mrad, and Y. Beuzard. 1990. Mouse β thalassemia, a model for the membrane defects of erythrocytes in the human disease. J. Biol. Chem. 265:20247-20251.
-
(1990)
J. Biol. Chem.
, vol.265
, pp. 20247-20251
-
-
Rouyer-Fessard, P.1
Leroy-Viard, K.2
Domenget, C.3
Mrad, A.4
Beuzard, Y.5
-
22
-
-
0026512776
-
Characterization and comparison of the red blood cell membrane damage in severe human α- and β-thalassemia
-
Advani, R., S. Sorenson, E. Shinar, W. Lande, E. Rachmilewitz, and S.L. Schrier. 1992. Characterization and comparison of the red blood cell membrane damage in severe human α-and β-thalassemia. Blood. 79:1058-1063.
-
(1992)
Blood
, vol.79
, pp. 1058-1063
-
-
Advani, R.1
Sorenson, S.2
Shinar, E.3
Lande, W.4
Rachmilewitz, E.5
Schrier, S.L.6
-
23
-
-
0024434530
-
Cellular and membrane properties of alpha and beta thalassemic erythrocytes are different: Implication for differences in clinical manifestations
-
Schrier, S., E. Rachmilewitz, and N. Mohandas. 1989. Cellular and membrane properties of alpha and beta thalassemic erythrocytes are different: implication for differences in clinical manifestations. Blood. 74:2194-2202.
-
(1989)
Blood
, vol.74
, pp. 2194-2202
-
-
Schrier, S.1
Rachmilewitz, E.2
Mohandas, N.3
-
24
-
-
4243714868
-
Deferiprone (L1) treatment removes erythrocyte membrane free iron and affects K-Cl cotransport activity in homozygous β thalassemia
-
De Franceschi, L., O. Shalev, A. Piga, M. Collell, O. Olivieri, R. Corrocher, R.P. Hebbel, N. Olivieri, and C. Brugnara. 1996. Deferiprone (L1) treatment removes erythrocyte membrane free iron and affects K-Cl cotransport activity in homozygous β thalassemia. Blood. 88 (Suppl.):24b.
-
(1996)
Blood
, vol.88
, Issue.SUPPL.
-
-
De Franceschi, L.1
Shalev, O.2
Piga, A.3
Collell, M.4
Olivieri, O.5
Corrocher, R.6
Hebbel, R.P.7
Olivieri, N.8
Brugnara, C.9
-
25
-
-
0026704541
-
Isolation, characterization, and immunuprecipitation studies of immune complexes from membranes of β-thalassemic erythrocytes
-
Yuan, J., R. Kannan, E. Shinar, E.A. Rachmilewitz, and P.S. Low. 1992. Isolation, characterization, and immunuprecipitation studies of immune complexes from membranes of β-thalassemic erythrocytes. Blood. 79:3007-3013.
-
(1992)
Blood
, vol.79
, pp. 3007-3013
-
-
Yuan, J.1
Kannan, R.2
Shinar, E.3
Rachmilewitz, E.A.4
Low, P.S.5
-
26
-
-
0029913286
-
Catalysis of soluble hemoglobin oxidation by free iron on sickle red cell membranes
-
Shalev, O., and R.P. Hebbel. 1996. Catalysis of soluble hemoglobin oxidation by free iron on sickle red cell membranes. Blood. 87:3948-3952.
-
(1996)
Blood
, vol.87
, pp. 3948-3952
-
-
Shalev, O.1
Hebbel, R.P.2
-
27
-
-
0024418244
-
The redox state of cysteines 201 and 317 of the erythrocyte anion exchanger is critical for ankyrin binding
-
Thevenin, B.J.-M., B.M. Willardson, and P.S. Low. 1989. The redox state of cysteines 201 and 317 of the erythrocyte anion exchanger is critical for ankyrin binding. J. Biol. Chem. 264:15886-15892.
-
(1989)
J. Biol. Chem.
, vol.264
, pp. 15886-15892
-
-
Thevenin, B.J.-M.1
Willardson, B.M.2
Low, P.S.3
-
28
-
-
0030058376
-
Long-term therapy with deferiprone
-
Olivieri, N. 1996. Long-term therapy with deferiprone. Acta Haematologica. 95:37-48.
-
(1996)
Acta Haematologica
, vol.95
, pp. 37-48
-
-
Olivieri, N.1
-
29
-
-
0026099699
-
Beyond hemoglobin polymerization: The red blood cell membrane and sickle disease pathophysiology
-
Hebbel, R.P. 1991. Beyond hemoglobin polymerization: the red blood cell membrane and sickle disease pathophysiology. Blood. 77:214-237.
-
(1991)
Blood
, vol.77
, pp. 214-237
-
-
Hebbel, R.P.1
|