Late onset familial dystonia: Could mitochondrial deficits induce a diffuse lesioning process of the whole basal ganglia system?

Journal of Neurology Neurosurgery and Psychiatry

Volumn 63, Issue 2, 1997, Pages 196-203

  Caparros Lefebvre, D ^a,c   Destee A ^b   Petit, H ^b  

^a Centre Hospitalier Universitaire Pointe a Pitre   (Guadeloupe)

^b LILLE UNIVERSITY HOSPITAL   (France)

^c University Hospital   (Guadeloupe)

Author keywords

Dysarthria; Familial dystonia; Mitochondrial disorders; Striatal necrosis

Indexed keywords

LACTIC ACID;

ADULT; ARTICLE; BASAL GANGLION; BRAIN NECROSIS; CEREBELLUM DISEASE; CEREBROSPINAL FLUID LEVEL; CLINICAL ARTICLE; CORPUS STRIATUM; DISORDERS OF MITOCHONDRIAL FUNCTIONS; DYSARTHRIA; DYSTONIA; ENZYME HISTOCHEMISTRY; FEMALE; FRONTAL LOBE; GAIT DISORDER; GLIOSIS; GLOBUS PALLIDUS; HUMAN; LACTATE BLOOD LEVEL; LEIGH DISEASE; MALE; MUSCLE BIOPSY; NEUROLOGIC DISEASE; NUCLEAR MAGNETIC RESONANCE IMAGING; ONSET AGE; OPTIC NERVE DISEASE; PARKINSONISM; PATHOPHYSIOLOGY; PEDUNCULAR ANSA; PRIORITY JOURNAL; RESPIRATORY CHAIN; STEREOTYPY; SUBSTANTIA NIGRA; SYMPTOM; THALAMUS;

EID: 0030813306     PISSN: 00223050     EISSN: None     Source Type: Journal    
DOI: 10.1136/jnnp.63.2.196     Document Type: Article

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