Dietary carnitine supplements slow disease progression in a putative mouse model for hereditary ceroid-lipofuscinosis

Journal of Neuroscience Research

Volumn 50, Issue 1, 1997, Pages 123-132

  Katz, Martin L ^a   Rice, Laura M ^a   Gao, Chun Lan ^a  

^a UNIVERSITY OF MISSOURI   (United States)

Author keywords

Animal model; Batten disease; Carnitine; Ceroid lipofuscinosis; Lysosomal storage; Neuronal degeneration

Indexed keywords

CARNITINE;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; AUTOSOMAL RECESSIVE DISORDER; BLINDNESS; CARNITINE DEFICIENCY; CHROMOSOME 1P; COGNITIVE DEFECT; CONTROLLED STUDY; DIET SUPPLEMENTATION; LYSOSOME STORAGE DISEASE; MALE; MOUSE; NERVE CELL DEGENERATION; NEURONAL CEROID LIPOFUSCINOSIS; NONHUMAN; PRIORITY JOURNAL; PSYCHOMOTOR DISORDER; RETINA DEGENERATION;

ANIMALS; BRAIN CHEMISTRY; CARNITINE; CEREBRAL CORTEX; DISEASE MODELS, ANIMAL; LYSOSOMES; MALE; MICE; MICE, INBRED C57BL; MICE, MUTANT STRAINS; MICROSCOPY, ELECTRON; NERVE DEGENERATION; NEURONAL CEROID-LIPOFUSCINOSES; NEURONS; RETINA; SURVIVAL ANALYSIS;

EID: 0030754261     PISSN: 03604012     EISSN: None     Source Type: Journal    
DOI: 10.1002/(SICI)1097-4547(19971001)50:1<123::AID-JNR13>3.0.CO;2-C     Document Type: Article

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