Treatment of thalassaemia major with phenylbutyrate and hydroxyurea [4]

Lancet

Volumn 350, Issue 9076, 1997, Pages 491-492

  Olivieri, N F ^a   Rees, D C ^a   Ginder, G D ^a   Thein, S L ^a   Brittenham, G M ^a   Waye, J S ^a   Weatherall, D J ^a  

^a HOSPITAL FOR SICK CHILDREN   (Canada)

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA GLOBIN; ARYLBUTYRIC ACID DERIVATIVE; GAMMA GLOBIN; HEMOGLOBIN A; HEMOGLOBIN F; HYDROXYUREA;

ADULT; CASE REPORT; ERYTHROCYTE TRANSFUSION; FEMALE; HUMAN; LETTER; MALE; ORAL DRUG ADMINISTRATION; PRIORITY JOURNAL; SCHOOL CHILD; THALASSEMIA MAJOR;

EID: 0030748791     PISSN: 01406736     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0140-6736(05)63080-2     Document Type: Article

References (5)

1. DJ Weatherall JB Clegg The thalassaemia syndromes 1981 Blackwell Scientific Publications Oxford
2. NF Olivieri Reactivation of fetal haemoglobin in patients with thalassaemia Sem Hematol 33 1996 24 42
3. JE Graig SM Sheerin R Barnetson SL Thein The molecular basis of HPFH in a British family identified by heteroduplex formation Br J Haematol 84 1993 106 110
4. M Sutton E Bouhassira R Nagel Polymerase chain reaction amplification applied to the determination of β-like globin haplotypes Am J Hematol 32 1989 66 69
5. P Rigano L Manfré R La Galla Clinical and hematological response to hydroxyurea in a patient with Hb Lepore/β-thalassaemia Hemoglobin 21 1997 219 226