Mitochondrial abnormalities in a murine model of primary carnitine deficiency

European Neurology

Volumn 38, Issue 4, 1997, Pages 302-309

  Kaido, M ^a   Fujimura, H ^a   Ono, A ^a   Toyooka, K ^a   Yoshikawa, H ^a   Nishimura, T ^a   Ozaki, K ^b   Narama, I ^b   Kuwajima, M ^a,c  

^a OSAKA UNIVERSITY MEDICAL SCHOOL   (Japan)

^b SETSUNAN UNIVERSITY   (Japan)

^c UNIVERSITY OF TOKUSHIMA   (Japan)

Author keywords

Juvenile visceral steatosis mouse; Mitochondrial abnormalities; Mn superoxide dismutase; Primary systemic carnitine deficiency; Replacement therapy

Indexed keywords

CARNITINE; ENZYME; LIPID; MANGANESE SUPEROXIDE DISMUTASE;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CARNITINE DEFICIENCY; CONTROLLED STUDY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME ACTIVITY; HEART MITOCHONDRION; HISTOGRAM; HOMOZYGOTE; IMMUNOHISTOCHEMISTRY; INTRAPERITONEAL DRUG ADMINISTRATION; KIDNEY; LIPID STORAGE; LIVER MITOCHONDRION; MOUSE; MUSCLE CELL; MUSCLE MITOCHONDRION; NERVOUS SYSTEM; NONHUMAN; OXIDATION; PATHOLOGY; PRIORITY JOURNAL; RESPIRATORY CHAIN; STEATOSIS; SUBSTITUTION THERAPY; SURVIVAL;

ANIMALS; BRAIN; CARNITINE; DISEASE MODELS, ANIMAL; DRUG EVALUATION, PRECLINICAL; ELECTRON TRANSPORT; MICE; MICE, INBRED C3H; MICROSCOPY, ELECTRON; MITOCHONDRIAL ENCEPHALOMYOPATHIES; MUSCLE, SKELETAL;

EID: 0030682077     PISSN: 00143022     EISSN: 14219913     Source Type: Journal    
DOI: 10.1159/000113399     Document Type: Article

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