Acylcarnitine removal in a patient with acyl-CoA β-oxidation deficiency disorder: Effect of L-carnitine therapy and starvation

Clinica Chimica Acta

Volumn 252, Issue 2, 1996, Pages 109-122

  Fontaine, Monique ^a   Briand, Gilbert ^a,b   Vallée, Louis ^a   Ricart, Guy ^b   Degand, Pierre ^a   Divry, Priscille ^c   Vianey Saban, Christine ^c   Vamecq, Joseph ^a  

^a LILLE UNIVERSITY HOSPITAL   (France)

^b UNIV LILLE   (France)

^c HÔPITAL DEBROUSSE   (France)

Author keywords

Acylcarnitine; Deficient mitochondrial oxidation; L Carnitine; Mass spectrometry; Starvation

Indexed keywords

ACYL COENZYME A DEHYDROGENASE; ACYLCARNITINE; CARNITINE; LEVOCARNIL; UNCLASSIFIED DRUG;

ARTICLE; BLOOD ANALYSIS; CASE REPORT; CHILD; CONTROLLED STUDY; ENZYME DEFICIENCY; FATTY ACID OXIDATION; GAS CHROMATOGRAPHY; HUMAN; HUMAN EXPERIMENT; MASS SPECTROMETRY; METABOLIC DISORDER; NORMAL HUMAN; ORAL DRUG ADMINISTRATION; PRIORITY JOURNAL; STARVATION; URINALYSIS;

EID: 0030606915     PISSN: 00098981     EISSN: None     Source Type: Journal    
DOI: 10.1016/0009-8981(96)06323-1     Document Type: Article

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