Evidence that lysosomal storage of proteolipids is a cell autonomous process in the motor neuron degeneration (mnd) mouse, a model of neuronal ceroid lipofuscinosis

Neuroscience Letters

Volumn 219, Issue 2, 1996, Pages 111-114

  Lipman, Ruth D ^a   Donohue, Leah R ^b   Hoppe, Peter ^b   Bronson, Roderick T ^a,b  

^a TUFTS UNIVERSITY   (United States)

^b JACKSON LABORATORY   (United States)

Author keywords

Bone marrow transplantation; Cell autonomous; Chimera; Mnd Mice; Neuronal ceroid lipofuscinosis; Proteolipid

Indexed keywords

LIPOFUSCIN; PROTEOLIPID;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BONE MARROW TRANSPLANTATION; CONTROLLED STUDY; LYSOSOME; MOTONEURON; MOUSE; MUTANT; NERVE DEGENERATION; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL;

AGING; ANIMALS; BONE MARROW TRANSPLANTATION; CHIMERA; DISEASE MODELS, ANIMAL; HIPPOCAMPUS; LYSOSOMES; MICE; MICE, INBRED BALB C; MICE, NEUROLOGIC MUTANTS; MOTOR NEURONS; NERVE DEGENERATION; NEURONAL CEROID-LIPOFUSCINOSES; PROTEOLIPIDS; RODENT DISEASES;

EID: 0030598372     PISSN: 03043940     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0304-3940(96)13185-2     Document Type: Article

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