Only sphingolipid activator protein B (SAP-B or saposin B) stimulates the degradation of globotriaosylceramide by recombinant human lysosomal α-galactosidase in a detergent-free liposomal system

FEBS Letters

Volumn 393, Issue 1, 1996, Pages 74-76

  Kase, Ryoichi ^a   Bierfreund, Uwe ^b   Klein, Andreas ^b   Kolter, Thomas ^b   Itoh, Kohji ^a   Suzuki, Minoru ^a   Hashimoto, Yasuhiro ^a   Sandhoff, Konrad ^b   Sakuraba, Hitoshi ^a  

^a TOKYO METROPOLITAN INSTITUTE OF MEDICAL SCIENCE   (Japan)

^b UNIVERSITY OF BONN   (Germany)

Author keywords

Globotriaosylceramide; Saposin B; Sphingolipid activator protein B; Galactosidase

Indexed keywords

ALPHA GALACTOSIDASE; GLOBOTRIAOSYLCERAMIDE; LIPOSOME; SPHINGOLIPID ACTIVATOR PROTEIN;

ARTICLE; ENZYME ACTIVITY; HUMAN; HYDROLYSIS; IN VITRO STUDY; LYSOSOME; PH; PHYSIOLOGY; PRIORITY JOURNAL; REACTION ANALYSIS;

EID: 0030576938     PISSN: 00145793     EISSN: None     Source Type: Journal    
DOI: 10.1016/0014-5793(96)00863-0     Document Type: Article

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