Differences in the Nonreducing Ends of Heparan Sulfates Excreted by Patients with Mucopolysaccharidoses Revealed by Bacterial Heparitinases: A New Tool for Structural Studies and Differential Diagnosis of Sanfilippo's and Hunter's Syndromes

Laboratory Investigation

Volumn 75, Issue 6, 1996, Pages 771-781

  Toma, Leny ^a   Dietrich, Carl P ^a   Nader, Helena B ^a  

^a FEDERAL UNIVERSITY OF SÃO PAULO   (Brazil)

Author keywords

[No Author keywords available]

Indexed keywords

ACETYL COENZYME A ACETYLTRANSFERASE; ALPHA N ACETYLGLUCOSAMINIDASE; DISACCHARIDE; GLUCOSAMINE SULFATE; GLYCOSAMINOGLYCAN; HEPARAN SULFATE; HEPARIN LYASE; IDURONATE 2 SULFATASE; N ACETYLGLUCOSAMINE; NITROUS ACID; TRISACCHARIDE; URONIC ACID;

ADOLESCENT; ADULT; ARTICLE; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; DIFFERENTIAL DIAGNOSIS; ELECTROPHORESIS; ENZYME DEGRADATION; ENZYME MECHANISM; ENZYME SPECIFICITY; FLAVOBACTERIUM; HUMAN; HUNTER SYNDROME; MUCOPOLYSACCHARIDOSIS; PRIORITY JOURNAL; SANFILIPPO SYNDROME; URINALYSIS; URINE LEVEL;

BIOLOGICAL MARKERS; CARBOHYDRATE SEQUENCE; CHONDROITIN SULFATES; DERMATAN SULFATE; DIAGNOSIS, DIFFERENTIAL; ELECTROPHORESIS, AGAR GEL; HEPARITIN SULFATE; HUMANS; MOLECULAR SEQUENCE DATA; MUCOPOLYSACCHARIDOSIS II; MUCOPOLYSACCHARIDOSIS III; POLYSACCHARIDE-LYASES; REFERENCE VALUES; SUBSTRATE SPECIFICITY;

EID: 0030476394     PISSN: 00236837     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

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