Brain MR imaging findings in two patients with Alpers' syndrome

Clinical Imaging

Volumn 20, Issue 4, 1996, Pages 235-237

  Smith, J K ^a   Mah, J K ^a   Castillo, M ^a,b  

^a UNIVERSITY OF NORTH CAROLINA SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF NORTH CAROLINA   (United States)

Author keywords

Alpers' syndrome; Liver disease; Neuronal degeneration; Progressive cerebral poliodystrophy

Indexed keywords

ALPER SYNDROME; ARTICLE; BRAIN ATROPHY; CASE REPORT; HUMAN; INFANT; LIVER DISEASE; MALE; NERVE CELL DEGENERATION; NUCLEAR MAGNETIC RESONANCE IMAGING; OCCIPITAL LOBE; PRESCHOOL CHILD;

EID: 0030265743     PISSN: 08997071     EISSN: None     Source Type: Journal    
DOI: 10.1016/0899-7071(95)00039-9     Document Type: Article

References (6)

1. 1. Harding BN. Progressive neuronal degeneration of childhood with liver disease (Alpers-Huttenlocher syndrome): a personal review. J Child Neurol 1990;5:273-287.
2. 2. Kendall BE, Boyd SG, Egger J, Harding BN. Progressive neuronal degeneration of childhood with liver disease. Computed tomographic features. Neuroradiology 1987;29:74-180.
3. 3. Alpers BJ. Diffuse progressive degeneration of the gray matter of the cerebrum. Arch Neurol Psychiatry 1931;25:469-505.
4. 4. Barkovich AJ, Good WV, Koch TK, Berg BO. Mitochondrial disorders: analysis of their clinical and imaging characteristics. AJNAR 1993;14:1119-1137.
5. 5. Tulina MH, Holme E, Kristiansson B, Larsson NG, Oldfors A. Mitochondrial encephalomyopathies in childhood. II. Clinical manifestations and syndromes. J Pediatr 1991;119:251-256.
6. 6. Manuelidis EE, Rorke LB. Transmission of Alpers disease (chronic progressive encephalopathy) produces experimental Creutzfeldt-Jakob disease in hamsters. Neurology 1989;39:615-621.