Antibody to C1-inhibitor in a patient receiving C1-inhibitor infusions for treatment of hereditary angioneurotic edema with systemic lupus erythematosus reacts with a normal allotype of residue 458 of C1-inhibitor

Journal of Laboratory and Clinical Medicine

Volumn 128, Issue 4, 1996, Pages 438-443

  Donaldson, V H ^a   Bissler, J J ^a   Welch, T R ^a   Burton, M F ^a   Davis III, A E ^a  

^a CINCINNATI CHILDREN S HOSPITAL RESEARCH FOUNDATION   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

EID: 0030257393     PISSN: 00222143     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0022-2143(96)80017-5     Document Type: Article

References (15)

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2. Haines A Lepow IH Studies on human C-1 esterase. II. Function of purified C1-esterase in the human complement system J Immunol 92 1964 468 478
3. Hauptmann G Grosshans E Heid E Lupus erythemateux aigu avec deficit complet de la fraction C4 du complement Nouv Presse Med 3 1974 881 882
4. Jackson CG Ochs HD Wedgwood RJ Immune response of a patient with deficiency of the fourth component of complement and systemic lupus erythematosus N Engl J Med 300 1979 1124 1129
5. Donaldson VH Hess EV McAdams AJ Lupus-erythematosus-like disease in three unrelated women with hereditary angioneurotic edema Ann Intern Med 86 1977 312 313
6. Bissler JJ Donaldson VH Davis AE III Contiguous deletion and duplication mutations resulting in type 1 hereditary angioneurotic edema Hum Genet 93 1994 265 269
7. Levy LR Lepow IH Assay and properties of serum inhibitor of C-1 esterase Proc Soc Exp Biol Med 101 1959 608 611
8. Mancini G Carbonara AO Heremans JF Immunochemical quantitation of antigens by single radial immunodiffusion Int J Immunochem 2 1965 235 254
9. Donaldson VH Bernstein DI Wagner CJ Angioneurotic edema with acquired C1 inhibitor deficiency and autoantibody to C1 inhibitor: response to plasmapheresis and cytotoxic therapy J Lab Clin Med 119 1992 397 406
10. Bock SC Skriver K Nielsen E Human C1 inhibitor: primary structure, cDNA cloning, and chromosomal localization Biochemistry 25 1986 4292 4301
11. Welch TR Beischel LS Choi EM Molecular genetics of C4B deficiency in IGA nephropathy Hum Immunol 26 1989 353 363
12. Cicardi M Bisiani G Cugno M Autoimmune C1 inhibitor deficiency: report of eight patients Am J Med 95 1993 169 175
13. Bork K Witzke G Long term prophylaxis with C1-inhibitor [C1-INH]concentrate in patients with recurrent angioedema caused by hereditary and acquired C1-inhibitor deficiency J Allergy Clin Immunol 83 1989 677 682
14. Donaldson VH Wagner CJ Davis AE III An autoantibody to C1-inhibitor recognizes the reactive center of the inhibitor J Lab Clin Med 127 1996 229 232
15. Donaldson VH Falconieri MW A modification of an affinity procedure for purification of human C1-inhibitor that provides a homogenous stable preparation J Immunol Methods 157 1993 101 104