-
1
-
-
0025868103
-
Demonstration that CFTR is a chloride channel by alteration of its anion selectivity
-
Anderson, M. P., R. J. Gregory, S. Thompson, D. W. Souza, S. Paul, R. C. Mulligan, A. E. Smith, and M. J. Welsh. Demonstration that CFTR is a chloride channel by alteration of its anion selectivity. Science Wash. DC 253: 202-205, 1991.
-
(1991)
Science Wash. DC
, vol.253
, pp. 202-205
-
-
Anderson, M.P.1
Gregory, R.J.2
Thompson, S.3
Souza, D.W.4
Paul, S.5
Mulligan, R.C.6
Smith, A.E.7
Welsh, M.J.8
-
2
-
-
0026651508
-
Chloride channels in the apical membrane of normal and cystic fibrosis airway and intestinal epithelia
-
Lung Cell. Mol. Physiol. 7
-
Anderson, M. P., D. N. Sheppard, H. A. Berger, and M. J. Welsh. Chloride channels in the apical membrane of normal and cystic fibrosis airway and intestinal epithelia. Am. J. Physiol. 263 (Lung Cell. Mol. Physiol. 7): L1-L14, 1992.
-
(1992)
Am. J. Physiol.
, vol.263
-
-
Anderson, M.P.1
Sheppard, D.N.2
Berger, H.A.3
Welsh, M.J.4
-
3
-
-
0025871551
-
Calcium and cAMP activate different chloride channels in the apical membrane of normal and cystic fibrosis epithelia
-
Anderson, M. P., and M. J. Welsh. Calcium and cAMP activate different chloride channels in the apical membrane of normal and cystic fibrosis epithelia. Proc. Natl. Acad. Sci. USA 88: 6003-6007, 1991.
-
(1991)
Proc. Natl. Acad. Sci. USA
, vol.88
, pp. 6003-6007
-
-
Anderson, M.P.1
Welsh, M.J.2
-
4
-
-
0026077676
-
Identification and regulation of the cystic fibrosis transmembrane conductance regulator-generated chloride channel
-
Berger, H. A., M. P. Anderson, R. J. Gregory, S. Thompson, P. W. Howard, R. A. Maurer, R. Mulligan, A. E. Smith, and M. J. Welsh. Identification and regulation of the cystic fibrosis transmembrane conductance regulator-generated chloride channel. J. Clin. Invest. 88: 1422-1431, 1991.
-
(1991)
J. Clin. Invest.
, vol.88
, pp. 1422-1431
-
-
Berger, H.A.1
Anderson, M.P.2
Gregory, R.J.3
Thompson, S.4
Howard, P.W.5
Maurer, R.A.6
Mulligan, R.7
Smith, A.E.8
Welsh, M.J.9
-
5
-
-
0025242929
-
Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis
-
Cheng, S. H., R. J. Gregory, J. Marshall, S. Paul, D. W. Souza, G. A. White, C. R. O'Riordan, and A. E. Smith. Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis. Cell 63: 827-834, 1990.
-
(1990)
Cell
, vol.63
, pp. 827-834
-
-
Cheng, S.H.1
Gregory, R.J.2
Marshall, J.3
Paul, S.4
Souza, D.W.5
White, G.A.6
O'Riordan, C.R.7
Smith, A.E.8
-
7
-
-
0025942250
-
Immunocytochemical localization of the cystic fibrosis gene product CFTR
-
Crawford, I., P. C. Maloney, P. L. Zeitlin, W. B. Guggino, S. C. Hyde, H. Turley, K. C. Gatter, A. Harris, and C. F. Higgins. Immunocytochemical localization of the cystic fibrosis gene product CFTR. Proc. Natl. Acad. Sci. USA 88: 9262-9266, 1991.
-
(1991)
Proc. Natl. Acad. Sci. USA
, vol.88
, pp. 9262-9266
-
-
Crawford, I.1
Maloney, P.C.2
Zeitlin, P.L.3
Guggino, W.B.4
Hyde, S.C.5
Turley, H.6
Gatter, K.C.7
Harris, A.8
Higgins, C.F.9
-
8
-
-
0028032866
-
Abnormal subcellular localization of mutated CFTR protein in a cystic fibrosis epithelial cell line
-
Demolombe, S., I. Baro, M. Laurent, A. S. Hongre, A. Pavirani, and D. Escande. Abnormal subcellular localization of mutated CFTR protein in a cystic fibrosis epithelial cell line. Eur. J. Cell Biol. 65: 214-219, 1994.
-
(1994)
Eur. J. Cell Biol.
, vol.65
, pp. 214-219
-
-
Demolombe, S.1
Baro, I.2
Laurent, M.3
Hongre, A.S.4
Pavirani, A.5
Escande, D.6
-
9
-
-
0027925829
-
Autosomal dominant polycystic kidney disease
-
Gabow, P. A. Autosomal dominant polycystic kidney disease. N. Engl. J. Med. 329:332-342, 1993.
-
(1993)
N. Engl. J. Med.
, vol.329
, pp. 332-342
-
-
Gabow, P.A.1
-
10
-
-
0028894081
-
In vitro fluid secretion by epithelium from polycystic kidneys
-
Grantham, J. J., M. Ye, V. H. Gattone II, and L. P. Sullivan. In vitro fluid secretion by epithelium from polycystic kidneys. J. Clin. Invest. 95: 195-202, 1995.
-
(1995)
J. Clin. Invest.
, vol.95
, pp. 195-202
-
-
Grantham, J.J.1
Ye, M.2
Gattone II, V.H.3
Sullivan, L.P.4
-
11
-
-
0025092468
-
Anion selectivity and block of the small-conductance chloride channel on pancreatic duct cells
-
Cell Physiol. 28
-
Gray, M. A., C. E. Pollard, A. Harris, L. Coleman, J. R. Greenwell, and B. E. Argent. Anion selectivity and block of the small-conductance chloride channel on pancreatic duct cells. Am. J. Physiol. 259 (Cell Physiol. 28): C752-C761, 1990.
-
(1990)
Am. J. Physiol.
, vol.259
-
-
Gray, M.A.1
Pollard, C.E.2
Harris, A.3
Coleman, L.4
Greenwell, J.R.5
Argent, B.E.6
-
12
-
-
0025114509
-
Expression and characterization of the cystic fibrosis transmembrane conductance regulator
-
Gregory, R. J., S. H. Cheng, D. P. Rich, J. Marshall, S. Paul, K Hehir, L. Ostedgaard, K. W. Klinger, M. J. Welsh, and A. E. Smith. Expression and characterization of the cystic fibrosis transmembrane conductance regulator. Nature Lond. 347: 382-386, 1990.
-
(1990)
Nature Lond.
, vol.347
, pp. 382-386
-
-
Gregory, R.J.1
Cheng, S.H.2
Rich, D.P.3
Marshall, J.4
Paul, S.5
Hehir, K.6
Ostedgaard, L.7
Klinger, K.W.8
Welsh, M.J.9
Smith, A.E.10
-
13
-
-
0028861577
-
Anion secretion by the inner medullary collecting duct. Evidence for involvement of the cystic fibrosis transmembrane conductance regulator
-
Husted, R. F., K. A. Volk, R. D. Sigmund, and J. B. Stokes. Anion secretion by the inner medullary collecting duct. Evidence for involvement of the cystic fibrosis transmembrane conductance regulator. J. Clin. Invest. 95: 644-650, 1995.
-
(1995)
J. Clin. Invest.
, vol.95
, pp. 644-650
-
-
Husted, R.F.1
Volk, K.A.2
Sigmund, R.D.3
Stokes, J.B.4
-
14
-
-
0029002967
-
Polycystic kidney disease: The complete structure of the PKD1 gene and its protein
-
International Polycystic Kidney Disease Consortium. Polycystic kidney disease: the complete structure of the PKD1 gene and its protein. Cell 81:289-298, 1995.
-
(1995)
Cell
, vol.81
, pp. 289-298
-
-
-
15
-
-
0027402791
-
Localization of the cystic fibrosis transmembrane conductance regulator in airway secretory glands
-
Jacquot, J., E. Puchelle, J. Hinnrasky, C. Fuchey, C. Bettinger, C. Spilmont, N. Bonnet, A. Dieterle, D. Dreyer, A. Pavirani, and W. Dalemans. Localization of the cystic fibrosis transmembrane conductance regulator in airway secretory glands. Eur. Respir. J. 6: 169-176, 1993.
-
(1993)
Eur. Respir. J.
, vol.6
, pp. 169-176
-
-
Jacquot, J.1
Puchelle, E.2
Hinnrasky, J.3
Fuchey, C.4
Bettinger, C.5
Spilmont, C.6
Bonnet, N.7
Dieterle, A.8
Dreyer, D.9
Pavirani, A.10
Dalemans, W.11
-
16
-
-
0027363212
-
Altered fluid transport across airway epithelium in cystic fibrosis
-
Jiang, C., W. E. Finkbeiner, J. H. Widdicombe, P. B. McCray, Jr., and S. S. Miller. Altered fluid transport across airway epithelium in cystic fibrosis. Science Wash. DC 262: 424-427, 1993.
-
(1993)
Science Wash. DC
, vol.262
, pp. 424-427
-
-
Jiang, C.1
Finkbeiner, W.E.2
Widdicombe, J.H.3
McCray Jr., P.B.4
Miller, S.S.5
-
17
-
-
0027767585
-
Autosomal dominant polycystic kidney disease: Localization of the second gene to chromosome 4q13-q23
-
Kimberling, W. J., S. Kumar, P. A. Gabow, J. B. Kenyon, C. J. Connolly, and S. Somlo. Autosomal dominant polycystic kidney disease: localization of the second gene to chromosome 4q13-q23. Genomics 18: 467-472, 1993.
-
(1993)
Genomics
, vol.18
, pp. 467-472
-
-
Kimberling, W.J.1
Kumar, S.2
Gabow, P.A.3
Kenyon, J.B.4
Connolly, C.J.5
Somlo, S.6
-
18
-
-
0028177033
-
- channels in principal cells via a cyclic adenosine monophosphate-dependent pathway
-
- channels in principal cells via a cyclic adenosine monophosphate-dependent pathway. J. Clin. Invest. 93: 829-837, 1994.
-
(1994)
J. Clin. Invest.
, vol.93
, pp. 829-837
-
-
Ling, B.N.1
Kokko, K.E.2
Eaton, D.C.3
-
19
-
-
0024830952
-
Renal epithelial fluid secretion and cyst growth: The role of cyclic AMP
-
Mangoo-Karim, R., M. E. Uchic, M. Grant, W. A. Shumate, J. P. Calvet, C. H. Park, and J. J. Grantham. Renal epithelial fluid secretion and cyst growth: the role of cyclic AMP. FASEB. J. 3: 2629-2632, 1989.
-
(1989)
FASEB. J.
, vol.3
, pp. 2629-2632
-
-
Mangoo-Karim, R.1
Uchic, M.E.2
Grant, M.3
Shumate, W.A.4
Calvet, J.P.5
Park, C.H.6
Grantham, J.J.7
-
20
-
-
0013537241
-
Renal epithelial cyst formation and enlargement in vitro: Dependence on cAMP
-
Mangoo-Karim, R., M. Uchic, C. Lechene, and J. J. Grantham. Renal epithelial cyst formation and enlargement in vitro: dependence on cAMP. Proc. Natl. Acad. Sci. USA 86: 6007-6011, 1989.
-
(1989)
Proc. Natl. Acad. Sci. USA
, vol.86
, pp. 6007-6011
-
-
Mangoo-Karim, R.1
Uchic, M.2
Lechene, C.3
Grantham, J.J.4
-
21
-
-
0028266280
-
Chloride channels in apical membrane of primary cultures of rabbit distal bright convoluted tubule
-
Renal Fluid Electrolyte Physiol. 35
-
Poncet, V., M. Taue, M. Bidet, and P. Poujeol. Chloride channels in apical membrane of primary cultures of rabbit distal bright convoluted tubule. Am. J. Physiol. 266 (Renal Fluid Electrolyte Physiol. 35): F543-F553, 1994.
-
(1994)
Am. J. Physiol.
, vol.266
-
-
Poncet, V.1
Taue, M.2
Bidet, M.3
Poujeol, P.4
-
22
-
-
0022410264
-
A highly polymorphic DNA marker linked to adult polycystic kidney disease on chromosome 16
-
Reeders, S. T., M. H. Breuning, K. E. Davies, R. D. Nicholls, A. P. Jarman, D. R. Higgs, P. L. Pearson, and D. J. Weatherall. A highly polymorphic DNA marker linked to adult polycystic kidney disease on chromosome 16. Nature Lond. 317: 542-544, 1985.
-
(1985)
Nature Lond.
, vol.317
, pp. 542-544
-
-
Reeders, S.T.1
Breuning, M.H.2
Davies, K.E.3
Nicholls, R.D.4
Jarman, A.P.5
Higgs, D.R.6
Pearson, P.L.7
Weatherall, D.J.8
-
23
-
-
0027966771
-
Both CFTR and outwardly rectifying chloride channels contribute to cAMP-stimulated whole cell chloride currents
-
Cell Physiol. 35
-
Schwiebert, E. M., T. Flotte, G. R. Cutting, and W. B. Guggino. Both CFTR and outwardly rectifying chloride channels contribute to cAMP-stimulated whole cell chloride currents. Am. J. Physiol 266 (Cell Physiol. 35): C1464-C1477, 1994.
-
(1994)
Am. J. Physiol
, vol.266
-
-
Schwiebert, E.M.1
Flotte, T.2
Cutting, G.R.3
Guggino, W.B.4
-
24
-
-
0026759418
-
+ channel regulators on cystic fibrosis transmembrane conductance regulator chloride currents
-
+ channel regulators on cystic fibrosis transmembrane conductance regulator chloride currents. J. Gen. Physiol. 100: 573-591, 1992.
-
(1992)
J. Gen. Physiol.
, vol.100
, pp. 573-591
-
-
Sheppard, D.N.1
Welsh, M.J.2
-
25
-
-
0021840516
-
The sulphonylurea receptor may be an ATP-sensitive potassium channel
-
Sturgess, N. C., M. L. Ashford, D. L. Cook, and C. N. Hales. The sulphonylurea receptor may be an ATP-sensitive potassium channel. Lancet 2: 474-475, 1985.
-
(1985)
Lancet
, vol.2
, pp. 474-475
-
-
Sturgess, N.C.1
Ashford, M.L.2
Cook, D.L.3
Hales, C.N.4
-
26
-
-
0001394794
-
Pathogenesis and cellular mechanisms of polycystic kidney disease
-
edited by R. Watson and V. M. Torres. Oxford, UK: Oxford Univ. Press. In press
-
Wilson, P. D. Pathogenesis and cellular mechanisms of polycystic kidney disease. In: Polycystic Kidney Disease, edited by R. Watson and V. M. Torres. Oxford, UK: Oxford Univ. Press. In press.
-
Polycystic Kidney Disease
-
-
Wilson, P.D.1
-
27
-
-
0022479887
-
A new method for studying human polycystic kidney disease epithelia in culture
-
Wilson, P. D., R. W. Schrier, R. D. Breckon, and P. A. Gabow. A new method for studying human polycystic kidney disease epithelia in culture. Kidney Int. 30: 371-378, 1986.
-
(1986)
Kidney Int.
, vol.30
, pp. 371-378
-
-
Wilson, P.D.1
Schrier, R.W.2
Breckon, R.D.3
Gabow, P.A.4
-
29
-
-
0024340307
-
A volume-sensitive chloride conductance in human colonic cell line T84
-
Cell Physiol. 25
-
Worrell, R. T., A. G. Butt, W. H. Cliff, and R. A. Frizzell. A volume-sensitive chloride conductance in human colonic cell line T84.Am. J. Physiol. 256 (Cell Physiol. 25): C1111-C1119, 1989.
-
(1989)
Am. J. Physiol.
, vol.256
-
-
Worrell, R.T.1
Butt, A.G.2
Cliff, W.H.3
Frizzell, R.A.4
-
30
-
-
0026595804
-
CFTR protein expression in primary and cultured epithelia
-
Zeitlin, P. L., I. Crawford, L. Lu, S. Woel, M. E. Cohen, M. Donowitz, M. H. Montrose, A. Hamosh, G. R. Cutting, D. Gruenert, R. Huganir, P. Maloney, and W. B. Guggino. CFTR protein expression in primary and cultured epithelia. Proc. Natl. Acad. Sci. USA 89: 344-347, 1992.
-
(1992)
Proc. Natl. Acad. Sci. USA
, vol.89
, pp. 344-347
-
-
Zeitlin, P.L.1
Crawford, I.2
Lu, L.3
Woel, S.4
Cohen, M.E.5
Donowitz, M.6
Montrose, M.H.7
Hamosh, A.8
Cutting, G.R.9
Gruenert, D.10
Huganir, R.11
Maloney, P.12
Guggino, W.B.13
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